Preferred Label : Marginal Zone Lymphoma;
NCIt synonyms : MZBCL;
NCIt related terms : marginal zone B-cell lymphoma; MZL; Marginal zone lymphoma, NOS;
NCIt definition : A usually indolent mature B-cell lymphoma, arising from the marginal zone of lymphoid
tissues. It is characterized by the presence of small to medium sized atypical lymphocytes.
It comprises three entities, according to the anatomic sites involved: extranodal
marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue, which affects
extranodal sites (most often stomach, lung, skin, and ocular adnexa); nodal marginal
zone B-cell lymphoma, which affects lymph nodes without evidence of extranodal disease;
and splenic marginal zone B-cell lymphoma, which affects the spleen and splenic hilar
lymph nodes, bone marrow, and often the peripheral blood.;
Alternative definition : NCI-GLOSS: An indolent (slow-growing) type of B-cell non-Hodgkin lymphoma that begins
forming in certain areas (the marginal zones) of lymph tissue. There are three types
based on whether it forms in the spleen, lymph nodes, or other lymphoid tissue that
contains a lot of B cells (a type of white blood cell).;
Neoplastic status : Malignant;
ICD-O code : 9699/3;
Codes from synonyms : CDR0000562555; CDR0000543124; CDR0000562554;
Origin ID : C4341;
UMLS CUI : C1367654;
Automatic exact mappings (from CISMeF team)
- Currated CISMeF NLP mapping
- Disease excludes abnormal cell
- Disease excludes normal cell origin
- Has associated anatomic sites
- Semantic type(s)
- UMLS correspondences (same concept)
- Validated automatic mappings to BTNT
- concept_is_in_subset
- disease_excludes_finding
- disease_has_abnormal_cell
- disease_has_finding
- disease_has_molecular_abnormality
- disease_has_normal_cell_origin
- disease_has_normal_tissue_origin
- disease_has_primary_anatomic_site
- disease_may_have_abnormal_cell
