Malignant Triton Tumor

Preferred Label : Malignant Triton Tumor;

NCIt synonyms : Malignant Neoplasm of Peripheral Nerve Sheath with Rhabdomyosarcoma; Malignant Neoplasm of the Peripheral Nerve Sheath with Rhabdomyosarcoma; Malignant Peripheral Nerve Sheath Neoplasm with Rhabdomyosarcoma; Malignant Tumor of Peripheral Nerve Sheath with Rhabdomyosarcoma; MPNST with Rhabdomyosarcoma; Malignant Tumor of the Peripheral Nerve Sheath with Rhabdomyosarcoma; Malignant Peripheral Nerve Sheath Tumor with Rhabdomyosarcoma;

NCIt related terms : Triton tumor, malignant;

NCIt definition : A malignant peripheral nerve sheath tumor which shows rhabdomyosarcomatous differentiation. More than half of the patients have neurofibromatosis type 1. The prognosis is usually poor.;

Neoplastic status : Malignant;

ICD-O code : 9561/3;

Details

Origin ID

C4335;

UMLS CUI

C0334616;

Automatic exact mappings (from CISMeF team)
- Malignant peripheral nerve sheath tumour with rhabdomyoblastic differentiation [ICD-11 Extension code]
- malignant triton tumor [DO Concept]
Currated CISMeF NLP mapping
- Malignant Triton tumor (disorder) [SNOMED CT concept]
- Malignant peripheral nerve sheath tumor with rhabdomyoblastic differentiation (morphologic abnormality) [SNOMED CT concept]
- Malignant triton tumor [ORDO Disease]
- triton tumor, malignant [SNOMED Notion]
DO Cross reference
- malignant triton tumor [DO Concept]
Disease excludes normal cell origin
- Epithelial Cell [NCIt concept]
Disease may have findings
- Aggressive Clinical Course [NCIt concept]
- Geographic Necrosis [NCIt concept]
Has associated anatomic sites
- Connective and Soft Tissue [NCIt concept]
- Nervous System [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Malignant Triton tumor (disorder) [SNOMED CT concept]
- Malignant peripheral nerve sheath tumor with rhabdomyoblastic differentiation (morphologic abnormality) [SNOMED CT concept]
- Malignant triton tumor [ORDO Disease]
- malignant triton tumor [DO Concept]
- triton tumor, malignant [SNOMED Notion]
concept_is_in_subset
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology Terminology [NCIt concept]
- Mapped ICDO3.1 Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology Terminology [NCIt concept]
- Mapped ICDO3.2 Terminology [NCIt concept]
- NCIt Neoplasm Core Terminology [NCIt concept]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
- Indolent Clinical Course [NCIt concept]
- Intermediate Filaments Present [NCIt concept]
- Intracytoplasmic Eosinophilic Inclusion [NCIt concept]
disease_excludes_normal_tissue_origin
- Epithelial Tissue [NCIt concept]
disease_has_abnormal_cell
- Hyperchromatic Spindle Cell [NCIt concept]
- Malignant Cell [NCIt concept]
- Malignant Perineural Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Neuroepithelial Cell and Neoplastic Perineural Cell [NCIt concept]
- Neoplastic Perineural Cell [NCIt concept]
disease_has_finding
- Diffuse Pattern [NCIt concept]
- Firm Mass [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
- Mesenchymal Differentiation [NCIt concept]
- Necrotic Change [NCIt concept]
- Pseudoencapsulated Mass [NCIt concept]
- Rhabdomyosarcomatous Differentiation [NCIt concept]
disease_has_normal_cell_origin
- Neuron, Neuroepithelial Cell, and Supporting Cell of the Nervous System [NCIt concept]
- Perineural Cell [NCIt concept]
disease_has_normal_tissue_origin
- Connective and Soft Tissue [NCIt concept]
- Nerve Tissue and Nerve Sheaths [NCIt concept]
- Nerve Tissue, Neuroepithelial Tissue, and Nerve Sheaths [NCIt concept]
disease_has_primary_anatomic_site
- Peripheral Nerve [NCIt concept]
disease_may_have_cytogenetic_abnormality
- Loss of Chromosome 22 [NCIt concept]
disease_may_have_molecular_abnormality
- TP53 Gene Inactivation [NCIt concept]

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