Malignant Glomus Tumor

Preferred Label : Malignant Glomus Tumor;

NCIt synonyms : Glomangiosarcoma; Malignant Glomus Neoplasm;

NCIt related terms : Glomus tumor, malignant;

NCIt definition : A very rare morphologic variant of glomus tumor with a size greater than 2 cm. The tumor arises in subfascial or visceral tissues. It is characterized by the presence of atypical mitotic figures, or marked nuclear atypia, or the combination of both. It has an aggressive clinical course.;

Neoplastic status : Malignant;

ICD-O code : 8710/3; 8711/3;

Details

Origin ID

C4221;

UMLS CUI

C1266111;

Automatic exact mappings (from CISMeF team)
- Glomangiosarcoma [ICD-9 code]
- Glomangiosarcoma [ICD-11 Extension code]
- glomangiosarcoma [DO Concept]
Currated CISMeF NLP mapping
- Glomangiosarcoma [ICD-O code]
- Glomangiosarcoma (morphologic abnormality) [SNOMED CT concept]
- Glomus tumor, malignant [ICD-O code]
- Glomus tumor, malignant (morphologic abnormality) [SNOMED CT concept]
- glomangiosarcoma [SNOMED Notion]
DO Cross reference
- glomangiosarcoma [DO Concept]
Disease excludes normal cell origin
- Neuron, Neuroepithelial Cell, and Supporting Cell of the Nervous System [NCIt concept]
Disease may have findings
- Aggressive Clinical Course [NCIt concept]
- Atypical Mitotic Figures [NCIt concept]
Excludes anatomical site(s)
- Bone [NCIt concept]
Has associated anatomic sites
- Connective and Soft Tissue [NCIt concept]
Has cytogenetic abnormalities
- NOTCH Gene Rearrangement [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Glomangiosarcoma [ICD-O code]
- Glomangiosarcoma (morphologic abnormality) [SNOMED CT concept]
- Glomus tumor, malignant [ICD-O code]
- Glomus tumor, malignant (morphologic abnormality) [SNOMED CT concept]
- glomangiosarcoma [DO Concept]
- glomangiosarcoma [SNOMED Notion]
concept_is_in_subset
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology Terminology [NCIt concept]
- Mapped ICDO3.1 Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology Terminology [NCIt concept]
- Mapped ICDO3.2 Terminology [NCIt concept]
- NCIt Neoplasm Core Terminology [NCIt concept]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
- Indolent Clinical Course [NCIt concept]
disease_has_abnormal_cell
- Glomus Cell [NCIt concept]
- Malignant Cell [NCIt concept]
- Malignant Connective and Soft Tissue Cell [NCIt concept]
- Malignant Glomus Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Connective and Soft Tissue Cell [NCIt concept]
disease_has_finding
- Malignant Cellular Infiltrate [NCIt concept]
- Perivascular Arrangement of Tumor Cells [NCIt concept]
disease_has_normal_cell_origin
- Connective and Soft Tissue Cell [NCIt concept]
- Pericyte [NCIt concept]
disease_has_normal_tissue_origin
- Connective and Soft Tissue [NCIt concept]
- Soft Tissue [NCIt concept]
disease_mapped_to_gene
- MIR143/NOTCH1 Fusion Gene [NCIt concept]
- MIR143/NOTCH2 Fusion Gene [NCIt concept]
- MIR143/NOTCH3 Fusion Gene [NCIt concept]
disease_may_have_molecular_abnormality
- BRAF Gene Mutation [NCIt concept]

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