Fibrolamellar Carcinoma

Preferred Label : Fibrolamellar Carcinoma;

NCIt synonyms : Polygonal Cell Type Hepatocellular Carcinoma with Fibrous Stroma; Hepatocellular Fibrolamellar Carcinoma; Fibrolamellar Carcinoma of the Liver Cells; Fibrolamellar Carcinoma of Liver Cells; Oncocytic Hepatocellular Tumor; Liver Cell Fibrolamellar Carcinoma; Fibrolamellar Hepatocellular Carcinoma; FLC;

NCIt related terms : Fibrolamellar Cancer; Hepatocellular carcinoma, fibrolamellar;

NCIt definition : A distinctive type of liver cell carcinoma that arises in non-cirrhotic livers and is seen predominantly in young patients. The tumor cells are polygonal and deeply eosinophilic, and are embedded in a fibrous stroma. The prognosis is similar to classical hepatocellular carcinoma that arises in non-cirrhotic livers, and better than hepatocellular carcinoma that arises in cirrhotic livers.;

Neoplastic status : Malignant;

ICD-O code : 8171/3;

Détails

Origin ID

C4131;

UMLS CUI

C0334287;

Automatic exact mappings (from CISMeF team)
- Fibrolamellar hepatocellular carcinoma [ORDO Disease]
- Hepatocellular carcinoma, fibrolamellar [ICD-11 Extension code]
- fibrolamellar carcinoma [DO Concept]
- fibrolamellar hepatocellular carcinoma [Radlex concept]
Currated CISMeF NLP mapping
- Fibrolamellar hepatocellular carcinoma [MeSH concept]
- Fibrolamellar hepatocellular carcinoma (disorder) [SNOMED CT concept]
- Hepatocellular carcinoma, fibrolamellar [ICD-O code]
- Hepatocellular carcinoma, fibrolamellar (morphologic abnormality) [SNOMED CT concept]
- fibrolamellar hepatocellular carcinoma [MeSH Supplementary Concept]
- hepatocellular carcinoma, fibrolamellar [SNOMED Notion]
DO Cross reference
- fibrolamellar carcinoma [DO Concept]
Disease excludes abnormal cell
- Malignant Squamous Cell [NCIt concept]
- Malignant Stromal Cell [NCIt concept]
- Neoplastic Smooth Muscle Cell [NCIt concept]
- Neoplastic Squamous Cell [NCIt concept]
Disease excludes normal cell origin
- Embryonic Cell [NCIt concept]
Excludes anatomical site(s)
- Extrahepatic Bile Duct [NCIt concept]
- Intrahepatic Bile Duct [NCIt concept]
Has associated anatomic sites
- Digestive System [NCIt concept]
- Hepatobiliary System [NCIt concept]
- Liver [NCIt concept]
Has cytogenetic abnormalities
- Loss of Chromosome 19 [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Fibrolamellar hepatocellular carcinoma [MeSH concept]
- Fibrolamellar hepatocellular carcinoma [ORDO Disease]
- Fibrolamellar hepatocellular carcinoma (disorder) [SNOMED CT concept]
- Hepatocellular carcinoma, fibrolamellar [ICD-O code]
- Hepatocellular carcinoma, fibrolamellar (morphologic abnormality) [SNOMED CT concept]
- fibrolamellar carcinoma [DO Concept]
- fibrolamellar hepatocellular carcinoma [MeSH Supplementary Concept]
- fibrolamellar type hepatocellular carcinoma [Disease (Nov.)]
- hepatocellular carcinoma, fibrolamellar [SNOMED Notion]
Validated automatic mappings to BTNT
- fibrolamellar type hepatocellular carcinoma [Disease (Nov.)]
concept_is_in_subset
- CPTAC Baseline Medical Forms Terminology [NCIt concept]
- CPTAC Liver Hepatocellular Carcinoma Baseline Form [NCIt concept]
- CPTAC Terminology [NCIt concept]
- CTRP Disease Terminology [NCIt concept]
- CTRP Terminology [NCIt concept]
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology Terminology [NCIt concept]
- Mapped ICDO3.1 Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology Terminology [NCIt concept]
- Mapped ICDO3.2 Terminology [NCIt concept]
- NCIt Neoplasm Core Terminology [NCIt concept]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
- Cirrhosis [NCIt concept]
- Favorable Clinical Outcome [NCIt concept]
- Intermediate Grade Neuroendocrine Lesion [NCIt concept]
- Low Grade Neuroendocrine Lesion [NCIt concept]
- Mixed Neoplastic Glandular and Squamous Cell Population [NCIt concept]
- Well Differentiated Neuroendocrine Lesion [NCIt concept]
disease_has_abnormal_cell
- Adenocarcinoma Cell [NCIt concept]
- Adenocarcinoma Cell with Eosinophilic Granular Cytoplasm [NCIt concept]
- Malignant Cell [NCIt concept]
- Malignant Epithelial Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Epithelial Cell [NCIt concept]
- Neoplastic Glandular Cell [NCIt concept]
- Polygonal Adenocarcinoma Cell with Eosinophilic Cytoplasm [NCIt concept]
disease_has_finding
- Carcinomatous Component Present [NCIt concept]
- Epithelial Component Present [NCIt concept]
- Lamellar Pattern [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
disease_has_normal_cell_origin
- Epithelial Cell [NCIt concept]
- Hepatocyte [NCIt concept]
disease_has_normal_tissue_origin
- Epithelial Tissue [NCIt concept]
- Hepatic Tissue [NCIt concept]
- Hepatobiliary Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Digestive System [NCIt concept]
- Hepatobiliary System [NCIt concept]
- Hepatopancreatobiliary System [NCIt concept]
- Liver [NCIt concept]
disease_mapped_to_gene
- DNAJB1/PRKACA Fusion Gene [NCIt concept]
disease_may_have_cytogenetic_abnormality
- Loss of Chromosome 19 [NCIt concept]
disease_may_have_molecular_abnormality
- DNAJB1-PRKACA Fusion Protein Expression [NCIt concept]
- PRKAR1A Gene Mutation [NCIt concept]
pathogenesis_of_disease_involves_gene
- DNAJB1/PRKACA Fusion Gene [NCIt concept]

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