Myelodysplastic Syndrome with Ring Sideroblasts

Preferred Label : Myelodysplastic Syndrome with Ring Sideroblasts;

NCIt synonyms : Pure Sideroblastic Anemia; RARS; MDS-RS; Refractory Anemia with Ring Sideroblasts;

NCIt related terms : Refractory Anemia with Ringed Sideroblasts;

NCIt definition : A myelodysplastic syndrome characterized by an anemia in which 15% or more of the erythroid precursors are ring sideroblasts. The ring sideroblast is an erythroid precursor in which one third or more of the nucleus is encircled by granules which are positive for iron stain. (WHO, 2001);

Neoplastic status : Malignant;

ICD-O code : 9982/3;

Codes from synonyms : D46.1;

Details

Origin ID

C4036;

UMLS CUI

C1264195;

Currated CISMeF NLP mapping
- Acquired idiopathic sideroblastic anemia [ORDO Disease]
- Refractory anaemia with ring sideroblasts [ICD-11 Category]
- Refractory anaemia with ringed sideroblasts [MedDRA Preferred Term]
- Refractory anemia with ring sideroblasts [ICD-10 Sub-category]
- Refractory anemia with ringed sideroblasts [HPO term]
- Refractory anemia with ringed sideroblasts [MedDRA LLT]
- Refractory anemia with ringed sideroblasts (disorder) [Inactive SNOMED CT concept]
- refractory anemia with ringed sideroblasts [Disease (Nov.)]
Disease may have findings
- Anisochromasia [NCIt concept]
- Chronic Clinical Course [NCIt concept]
- Hypercellular Bone Marrow [NCIt concept]
Has associated anatomic sites
- Bone Marrow [NCIt concept]
- Hematopoietic and Lymphatic System [NCIt concept]
See also inter- (CISMeF)
- primary acquired sideroblastic anemia [Disease (Nov.)]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Acquired idiopathic sideroblastic anemia [ORDO Disease]
- Myelodysplastic syndrome with ringed sideroblasts [MedDRA Preferred Term]
- Refractory anaemia with ring sideroblasts [ICD-11 Category]
- Refractory anaemia with ringed sideroblasts [MedDRA LLT]
- Refractory anaemia with ringed sideroblasts [MedDRA Preferred Term]
- Refractory anemia with ring sideroblasts [ICD-10 Sub-category]
- Refractory anemia with ringed sideroblasts [MedDRA LLT]
- Refractory anemia with ringed sideroblasts [HPO term]
- Refractory anemia with ringed sideroblasts (disorder) [Inactive SNOMED CT concept]
- refractory anemia with ringed sideroblasts [Disease (Nov.)]
concept_is_in_subset
- CTRP Disease Terminology [NCIt concept]
- CTRP Terminology [NCIt concept]
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology Terminology [NCIt concept]
- Mapped ICDO3.1 Terminology [NCIt concept]
- mCode Cancer Disorder Value Set [NCIt concept]
- mCode Primary Cancer Disorder Value Set [NCIt concept]
- mCode Primary Malignant Neoplasm Disorder Value Set [NCIt concept]
- mCode Terminology [NCIt concept]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
- Thrombocytosis [NCIt concept]
disease_has_abnormal_cell
- Neoplastic Cell [NCIt concept]
disease_has_finding
- Bone Marrow Dysplasia Present [NCIt concept]
- Erythroid Hyperplasia [NCIt concept]
- Ineffective Hematopoiesis [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
- Myeloblasts Under 1 Percent of Peripheral Blood White Cells [NCIt concept]
- Myeloblasts Under 20 Percent of Bone Marrow Nucleated Cells [NCIt concept]
- Myeloblasts Under 20 Percent of Peripheral Blood White Cells [NCIt concept]
- Myeloblasts Under 5 Percent of Bone Marrow Nucleated Cells [NCIt concept]
- Ring Sideroblasts 15 Percent or More of Erythroid Precursors [NCIt concept]
disease_has_primary_anatomic_site
- Bone Marrow [NCIt concept]
- Hematopoietic and Lymphatic System [NCIt concept]

Keyword's position in hierarchy(ies) :

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