Vulvar Paget Disease

Preferred Label : Vulvar Paget Disease;

NCIt synonyms : Vulvar Paget's Disease; Paget's Disease of Vulva; Vulva Paget's Disease; Paget's Disease of the Vulva; Vulvar Paget s Disease;

NCIt related terms : Paget Disease of the Vulva;

NCIt definition : An uncommon intraepithelial malignant neoplasm of eccrine or apocrine origin, arising from the vulva. It usually affects post-menopausal women. In approximately 10-20% of the cases there is an associated anorectal, or urothelial carcinoma or a skin appendage adenocarcinoma identified. It presents as a red, eczematous lesion. Microscopically, it is characterized by the presence of the typical Paget cells which are large, round cells with abundant pale cytoplasm and large nuclei with prominent nucleoli.;

Neoplastic status : Malignant;

Details

Origin ID

C4027;

UMLS CUI

C1275217;

Automatic exact mappings (from CISMeF team)
- Bowen's disease of vulva (disorder) [SNOMED CT concept]
- Crohn's disease of vulva (disorder) [SNOMED CT concept]
- vulval Paget's disease [DO Concept]
Currated CISMeF NLP mapping
- Paget disease of the vulva [Disease (Nov.)]
- Paget's disease of the vulva [MedDRA Preferred Term]
- Paget's disease of vulva (disorder) [SNOMED CT concept]
- Vulval Paget's disease (disorder) [Inactive SNOMED CT concept]
- Vulvar Paget disease [ICD-11 Sub-sub category]
DO Cross reference
- vulval Paget's disease [DO Concept]
Disease excludes abnormal cell
- Malignant Squamous Cell [NCIt concept]
- Malignant Stromal Cell [NCIt concept]
- Neoplastic Smooth Muscle Cell [NCIt concept]
- Neoplastic Squamous Cell [NCIt concept]
Disease may have findings
- Eczema [NCIt concept]
Excludes anatomical site(s)
- Breast [NCIt concept]
Has associated anatomic sites
- Female Reproductive System [NCIt concept]
- Genitourinary System [NCIt concept]
- Integumentary System [NCIt concept]
- Reproductive System [NCIt concept]
- Skin [NCIt concept]
- Vulva [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Paget disease of the vulva [Disease (Nov.)]
- Paget's disease of the vulva [MedDRA Preferred Term]
- Paget's disease of vulva (disorder) [SNOMED CT concept]
- Vulval Paget's disease (disorder) [Inactive SNOMED CT concept]
- vulval Paget's disease [DO Concept]
concept_is_in_subset
- CTRP Disease Terminology [NCIt concept]
- CTRP Terminology [NCIt concept]
- NCIt Neoplasm Core Terminology [NCIt concept]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
- Mixed Neoplastic Glandular and Squamous Cell Population [NCIt concept]
disease_has_abnormal_cell
- Adenocarcinoma Cell [NCIt concept]
- Malignant Cell [NCIt concept]
- Malignant Epithelial Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Epithelial Cell [NCIt concept]
- Neoplastic Glandular Cell [NCIt concept]
- Paget Cell [NCIt concept]
disease_has_finding
- Adnexal Differentiation [NCIt concept]
- Carcinomatous Component Present [NCIt concept]
- Cutaneous Involvement [NCIt concept]
- Epithelial Component Present [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
disease_has_normal_cell_origin
- Epithelial Cell [NCIt concept]
disease_has_normal_tissue_origin
- Epithelial Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Exocrine System [NCIt concept]
- Female Reproductive System [NCIt concept]
- Genitourinary System [NCIt concept]
- Skin [NCIt concept]
- Sweat Gland [NCIt concept]
- Vulva [NCIt concept]
may_be_associated_disease_of_disease
- Vulvar Apocrine Adenocarcinoma [NCIt concept]

Keyword's position in hierarchy(ies) :

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