NCIt definition : A sex cord-stromal tumor of the testis or the ovary. It is characterized by the presence
of Sertoli cells forming tubules. Leydig cells are rare or absent. It may be associated
with Peutz-Jeghers syndrome. In males, the presenting symptom is a slow growing testicular
mass. Most cases follow a benign clinical course. In females it may present with estrogenic
or androgenic manifestations. The vast majority of cases have a benign clinical course.;
Alternative definition : NICHD: A sex cord-stromal tumor of the testis or the ovary. It is characterized by
the presence of Sertoli cells forming tubules. Leydig cells are rare or absent. It
may be associated with Peutz-Jeghers syndrome.;