Pulmonary Blastoma

Preferred Label : Pulmonary Blastoma;

NCIt synonyms : Pneumoblastoma; Lung Blastoma; Blastoma of the Lung; Blastoma of Lung;

NCIt definition : A biphasic tumor that consists of fetal adenocarcinoma (typically low-grade) and primitive mesenchymal stroma. Foci of specific mesenchymal differentiation (osteosarcoma, chondrosarcoma, or rhabdomyosarcoma) may also be present, but are not required for the diagnosis. Most patients are smokers. The prognosis is very poor. (WHO 2015);

Neoplastic status : Malignant;

ICD-O code : 8972/3;

Details

Origin ID

C3732;

UMLS CUI

C0206629;

Automatic exact mappings (from CISMeF team)
- Pulmonary blastoma [ICD-11 Extension code]
Currated CISMeF NLP mapping
- Pulmonary blastoma [ICD-O code]
- Pulmonary blastoma [ORDO Disease]
- Pulmonary blastoma (disorder) [SNOMED CT concept]
- Pulmonary blastoma (morphologic abnormality) [SNOMED CT concept]
- pulmonary blastoma [DO Concept]
- pulmonary blastoma [Disease (Nov.)]
- pulmonary blastoma [MeSH Descriptor]
- pulmonary blastoma [MeSH concept]
- pulmonary blastoma [SNOMED Notion]
- pulmonary blastoma [Radlex concept]
DO Cross reference
- pulmonary blastoma [DO Concept]
Disease excludes abnormal cell
- Malignant Epithelial Small Cell [NCIt concept]
- Malignant Stromal Cell [NCIt concept]
- Neoplastic Smooth Muscle Cell [NCIt concept]
Disease may have findings
- Aggressive Clinical Course [NCIt concept]
- Cough [NCIt concept]
- Dyspnea [NCIt concept]
- Fever [NCIt concept]
- Hemoptysis [NCIt concept]
Excludes anatomical site(s)
- Neck [NCIt concept]
- Skin [NCIt concept]
HPO term
- Pleuropulmonary blastoma [HPO term]
Has associated anatomic sites
- Lung [NCIt concept]
- Respiratory System [NCIt concept]
- Thoracic Cavity [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Pulmonary blastoma [ICD-O code]
- Pulmonary blastoma [ORDO Disease]
- Pulmonary blastoma (disorder) [SNOMED CT concept]
- Pulmonary blastoma (morphologic abnormality) [SNOMED CT concept]
- pulmonary blastoma [Radlex concept]
- pulmonary blastoma [DO Concept]
- pulmonary blastoma [Disease (Nov.)]
- pulmonary blastoma [MeSH concept]
- pulmonary blastoma [MeSH Descriptor]
- pulmonary blastoma [SNOMED Notion]
concept_is_in_subset
- Cellosaurus Disease Terminology [NCIt concept]
- Cellosaurus Terminology [NCIt concept]
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology Terminology [NCIt concept]
- Mapped ICDO3.1 Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology Terminology [NCIt concept]
- Mapped ICDO3.2 Terminology [NCIt concept]
- NCIt Neoplasm Core Terminology [NCIt concept]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
- Premalignant Lesion [NCIt concept]
disease_excludes_molecular_abnormality
- DICER1 Gene Mutation [NCIt concept]
disease_has_abnormal_cell
- Malignant Cell [NCIt concept]
- Malignant Epithelial Cell [NCIt concept]
- Malignant Epithelial Spindle Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Epithelial Cell [NCIt concept]
disease_has_finding
- Anaplastic Lesion [NCIt concept]
- Biphasic Pattern [NCIt concept]
- Carcinomatous Component Present [NCIt concept]
- Epithelial Component Present [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
- Poorly Differentiated Lesion [NCIt concept]
- Primitive Mesenchymal Stroma Formation [NCIt concept]
- Tubular Structures of Glycogen-Rich Non-Ciliated Cells Present [NCIt concept]
disease_has_normal_cell_origin
- Epithelial Cell [NCIt concept]
disease_has_normal_tissue_origin
- Epithelial Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Lung [NCIt concept]
disease_mapped_to_gene
- TP53 Gene [NCIt concept]
disease_may_have_molecular_abnormality
- CTNNB1 Gene Mutation [NCIt concept]
- TP53 Gene Inactivation [NCIt concept]

Keyword's position in hierarchy(ies) :

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