Solid Pseudopapillary Neoplasm of the Pancreas

Preferred Label : Solid Pseudopapillary Neoplasm of the Pancreas;

NCIt synonyms : Solid Pseudopapillary Tumor of the Pancreas;

NCIt definition : A low-grade malignant neoplasm that arises from the exocrine pancreas. It is characterized by the presence of uniform cells that form solid and pseudopapillary patterns, cystic changes, and hemorrhage. Perineural invasion, vascular invasion, and invasion into surrounding tissues may be present. It usually presents as an encapsulated, solitary, and lobulated pancreatic mass. It is usually found incidentally during physical examination or it may present with abdominal discomfort and pain. It occurs predominantly in young women. Complete removal of the tumor is curative in the majority of cases.;

Neoplastic status : Malignant;

Details

Origin ID

C37212;

UMLS CUI

C1336030;

Automatic exact mappings (from CISMeF team)
- Solid pseudopapillary carcinoma of pancreas [ORDO Disease]
- Solid pseudopapillary neoplasm of pancreas [ICD-11 Extension code]
- Solid pseudopapillary tumor of the pancreas [MedDRA LLT]
Disease may have findings
- Encapsulated Mass [NCIt concept]
- Perineural Invasion [NCIt concept]
- Tumor Vascular Invasion [NCIt concept]
Has associated anatomic sites
- Digestive System [NCIt concept]
- Pancreas [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Solid pseudopapillary tumor of the pancreas [MedDRA LLT]
- Solid pseudopapillary tumour of the pancreas [MedDRA Preferred Term]
concept_is_in_subset
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology Terminology [NCIt concept]
- Mapped ICDO3.2 Terminology [NCIt concept]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
disease_has_abnormal_cell
- Malignant Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
disease_has_finding
- Cystic Change [NCIt concept]
- Hemorrhagic Change [NCIt concept]
- Lobulated Growth Pattern [NCIt concept]
- Low Grade Lesion [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
- Necrotic Change [NCIt concept]
- Pseudopapillary Pattern [NCIt concept]
disease_has_grade
- Low Grade [NCIt concept]
disease_has_primary_anatomic_site
- Exocrine Pancreas [NCIt concept]
disease_mapped_to_gene
- CTNNB1 Gene [NCIt concept]
disease_may_have_molecular_abnormality
- CTNNB1 Gene Mutation [NCIt concept]

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