Lymphomatoid Papulosis

Preferred Label : Lymphomatoid Papulosis;

NCIt synonyms : LyP;

NCIt definition : A chronic, recurrent cutaneous disorder characterized by the presence of spontaneously regressing papules. The papules are composed of an atypical lymphocytic infiltrate that contains anaplastic CD30-positive T-cells, which are found in type A and diffuse large cell type (type C) lymphomatoid papulosis. In a small number of cases, of type B, the lymphocytic infiltrate is composed of small, cerebriform-like lymphocytes that are often negative for CD30. The majority of cases follow a benign clinical course, but some cases are clonal and may progress to lymphoma. Treatment options include low dose methotrexate and psoralen/UVA (PUVA).;

Neoplastic status : Uncertain Malignant Potential;

ICD-O code : 9718/1;

Details

Origin ID

C3721;

UMLS CUI

C0206182;

Currated CISMeF NLP mapping
- Lymphomatoid papulosis [PASCAL descriptor]
- Lymphomatoid papulosis [ICD-10 Sub-category (who)]
- Lymphomatoid papulosis [MedDRA Preferred Term]
- Lymphomatoid papulosis [ORDO Disease]
- Lymphomatoid papulosis (disorder) [SNOMED CT concept]
- Lymphomatoid papulosis (morphologic abnormality) [SNOMED CT concept]
- lymphomatoid papulosis [Disease (Nov.)]
- lymphomatoid papulosis [MeSH Descriptor]
- lymphomatoid papulosis [MeSH concept]
Disease excludes abnormal cell
- Neoplastic B-Lymphocyte [NCIt concept]
Disease excludes normal cell origin
- Myeloid Cell [NCIt concept]
- Precursor Natural Killer Cell [NCIt concept]
- Precursor T-Lymphoblast [NCIt concept]
Disease may have findings
- Indolent Clinical Course [NCIt concept]
- Papular Lesion [NCIt concept]
- Skin Nodule [NCIt concept]
Has associated anatomic sites
- Hematopoietic and Lymphatic System [NCIt concept]
- Integumentary System [NCIt concept]
- Skin [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Lymphomatoid papulosis [ORDO Disease]
- Lymphomatoid papulosis [PASCAL descriptor]
- Lymphomatoid papulosis [ICD-10 Sub-category (who)]
- Lymphomatoid papulosis [MedDRA Preferred Term]
- Lymphomatoid papulosis (disorder) [SNOMED CT concept]
- Lymphomatoid papulosis (morphologic abnormality) [SNOMED CT concept]
- lymphomatoid papulosis [Disease (Nov.)]
- lymphomatoid papulosis [MeSH concept]
- lymphomatoid papulosis [MeSH Descriptor]
concept_is_in_subset
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- NCIt Neoplasm Core Terminology [NCIt concept]
disease_has_abnormal_cell
- Abnormal Hematopoietic and Lymphoid Cell [NCIt concept]
- Abnormal Lymphocyte [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Hematopoietic and Lymphoid Cell [NCIt concept]
- Neoplastic Lymphocyte [NCIt concept]
- Neoplastic T-Lymphocyte [NCIt concept]
- Neoplastic T-Lymphocyte and Neoplastic Natural Killer Cell [NCIt concept]
disease_has_finding
- Borderline Lesion [NCIt concept]
- CD30-Positive Neoplastic Cells Present [NCIt concept]
- Complete Regression [NCIt concept]
- Cutaneous Involvement [NCIt concept]
- Favorable Clinical Outcome [NCIt concept]
- Primary Lesion [NCIt concept]
disease_has_normal_cell_origin
- Activated Skin-Homing T-Lymphocyte [NCIt concept]
- Hematopoietic and Lymphoid Cell [NCIt concept]
- Lymphocyte [NCIt concept]
- Peripheral (Post-Thymic) T-Lymphocyte and Natural Killer Cell [NCIt concept]
- T-Lymphocyte and Natural Killer Cell [NCIt concept]
disease_has_normal_tissue_origin
- Hematopoietic and Lymphoid Tissue [NCIt concept]
- Lymphoid Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Hematopoietic and Lymphatic System [NCIt concept]
- Lymphatic System [NCIt concept]
- Skin [NCIt concept]
disease_may_have_cytogenetic_abnormality
- Clonal T-Cell Receptor Beta Chain Gene Rearrangement [NCIt concept]
- Clonal T-Cell Receptor Gamma Chain Gene Rearrangement [NCIt concept]
disease_may_have_molecular_abnormality
- Clonal T-Cell Receptor Beta Chain Gene Rearrangement [NCIt concept]
- Clonal T-Cell Receptor Gamma Chain Gene Rearrangement [NCIt concept]
may_be_associated_disease_of_disease
- Pityriasis Lichenoides et Varioliformis Acuta [NCIt concept]

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