Acute Myeloid Leukemia with t(11;17)(q23;q21); ZBTB16-RARA - CISMeF
Acute Myeloid Leukemia with t(11;17)(q23;q21); ZBTB16-RARANCIt concept
Preferred Label : Acute Myeloid Leukemia with t(11;17)(q23;q21); ZBTB16-RARA;
NCIt synonyms : Acute Promyelocytic Leukemia with t(11;17)(q23;q21); PLZF-RARA; Acute Promyelocytic Leukemia with t(11;17)(q23;q21); ZBTB16-RARA; Acute Promyelocytic Leukemia with t 11 17 q23 q21; Acute Promyelocytic Leukemia with t(11;17)(q23;q21); ZBTB16::RARA; Acute Myeloid Leukemia with t(11;17)(q23;q21); Acute Myeloid Leukemia with t(11;17)(q23;q21); ZBTB16::RARA; Acute Myeloid Leukemia with t(11;17)(q23;q21); ZBTB16::RARA Fusion; Acute Myeloid Leukemia with t(11;17)(q23;q21); ZBTB16-RARA Fusion;
NCIt related terms : APL with t(11;17)(q23;q21); ZBTB16-RARA; APL with t(11;17)(q23;q21); PLZF-RARA;
NCIt definition : Acute myeloid leukemia with the variant RARA t(11;17)(q23;q21) and the expression
of ZBTB16-RARA fusion protein. It lacks differentiation response to retinoids treatment.;
Alternative definition : NICHD: Acute myeloid leukemia with the variant RARA t(11;17)(q23;q21) and the expression
of PLZF-RARA fusion protein. It does not respond to retinoid treatment.;