Pagetoid Reticulosis

Preferred Label : Pagetoid Reticulosis;

NCIt definition : A variant of mycosis fungoides, characterized by an exclusively intraepidermal atypical (cerebriform) lymphocytic infiltrate. Patients present with a localized psoriasiform or hyperkeratotic patch or plaque, usually in the extremities. Extracutaneous dissemination of the disease has never been reported.;

Neoplastic status : Malignant;

Details

Origin ID

C35794;

UMLS CUI

C1367970;

Automatic exact mappings (from CISMeF team)
- Mycosis fungoides [ICD-11 Category]
- Mycosis fungoides (morphologic abnormality) [SNOMED CT concept]
- Pagetoid reticulosis [ICD-11 More detail]
- mycosis fungoides [SNOMED Notion]
Currated CISMeF NLP mapping
- pagetoid reticulosis [MeSH Descriptor]
- pagetoid reticulosis [MeSH concept]
Disease excludes abnormal cell
- Lymphocyte Predominant Cell [NCIt concept]
- Neoplastic B-Lymphocyte [NCIt concept]
- Reed-Sternberg Cell [NCIt concept]
Disease excludes normal cell origin
- Myeloid Cell [NCIt concept]
- Plasma Cell [NCIt concept]
- Precursor Natural Killer Cell [NCIt concept]
- Precursor T-Lymphoblast [NCIt concept]
Disease may have findings
- Chronic Clinical Course [NCIt concept]
- Dermatopathic Lymphadenopathy [NCIt concept]
- Pautrier Microabscess Present [NCIt concept]
- Progressive Disease [NCIt concept]
- Scaly Skin Eruption [NCIt concept]
- Single Cell Exocytosis [NCIt concept]
- Skin Patch [NCIt concept]
- Skin Plaque [NCIt concept]
Excludes anatomical site(s)
- Lymph Node [NCIt concept]
False automatic mappings
- Pagetoid reticulosis (disorder) [SNOMED CT concept]
- Pagetoid reticulosis (morphologic abnormality) [SNOMED CT concept]
Has associated anatomic sites
- Hematopoietic and Lymphatic System [NCIt concept]
- Integumentary System [NCIt concept]
- Skin [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Pagetoid reticulosis (disorder) [SNOMED CT concept]
- Pagetoid reticulosis (morphologic abnormality) [SNOMED CT concept]
- pagetoid reticulosis [MeSH concept]
- pagetoid reticulosis [MeSH Descriptor]
concept_is_in_subset
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
disease_excludes_finding
- Aggressive Clinical Course [NCIt concept]
- Benign Cellular Infiltrate [NCIt concept]
- Extracutaneous Dissemination of Disease [NCIt concept]
disease_has_abnormal_cell
- Abnormal Lymphocyte [NCIt concept]
- Cerebriform Lymphocyte [NCIt concept]
- Malignant Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Hematopoietic and Lymphoid Cell [NCIt concept]
- Neoplastic Lymphocyte [NCIt concept]
- Neoplastic T-Lymphocyte [NCIt concept]
- Neoplastic T-Lymphocyte and Neoplastic Natural Killer Cell [NCIt concept]
disease_has_finding
- Cutaneous Involvement [NCIt concept]
- Epidermotropic Lymphocytic Infiltrate [NCIt concept]
- Extranodal Disease [NCIt concept]
- Localized Skin Lesion [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
- Rare Lesion [NCIt concept]
disease_has_normal_cell_origin
- Hematopoietic and Lymphoid Cell [NCIt concept]
- Lymphocyte [NCIt concept]
- Peripheral (Post-Thymic) T-Lymphocyte [NCIt concept]
- Peripheral (Post-Thymic) T-Lymphocyte and Natural Killer Cell [NCIt concept]
- Peripheral Epidermotropic T-Lymphocyte [NCIt concept]
- T-Lymphocyte and Natural Killer Cell [NCIt concept]
disease_has_normal_tissue_origin
- Hematopoietic and Lymphoid Tissue [NCIt concept]
- Lymphoid Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Hematopoietic and Lymphatic System [NCIt concept]
- Lymphatic System [NCIt concept]
- Skin [NCIt concept]
disease_may_have_molecular_abnormality
- CDKN2A Gene Inactivation [NCIt concept]
- Clonal T-Cell Receptor Beta Chain Gene Rearrangement [NCIt concept]
- Clonal T-Cell Receptor Gamma Chain Gene Rearrangement [NCIt concept]
- PTEN Gene Inactivation [NCIt concept]

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