Inclusion Body Fibromatosis

Preferred Label : Inclusion Body Fibromatosis;

NCIt synonyms : Reye's Tumor; Digital Fibrous Tumor of Reye; Reye Tumor; Infantile Digital Fibromatosis; Infantile Digital Fibroma/Fibromatosis;

NCIt definition : A rare benign neoplasm arising from the soft tissues of the digits, in young children. It is characterized by the presence of fibroblastic spindle cells, and intracytoplasmic eosinophilic spherical inclusions.;

Neoplastic status : Benign;

Details

Origin ID

C3456;

UMLS CUI

C1318562;

Automatic exact mappings (from CISMeF team)
- Adenolymphoma (disorder) [SNOMED CT concept]
- Adenolymphoma (morphologic abnormality) [SNOMED CT concept]
- Askin tumor (morphologic abnormality) [SNOMED CT concept]
- Askin's tumor [MedDRA LLT]
- B-cell type acute leukaemia [MedDRA Preferred Term]
- Burkitt lymphoma (morphologic abnormality) [SNOMED CT concept]
- Burkitt's lymphoma (disorder) [SNOMED CT concept]
- Burkitt's tumor [MedDRA LLT]
- Castleman Disease [MeSH Descriptor]
- Chondroblastoma (morphologic abnormality) [SNOMED CT concept]
- Eccrine dermal cylindroma of skin (disorder) [SNOMED CT concept]
- Ewing's sarcoma [MedDRA Preferred Term]
- Ewing's sarcoma (morphologic abnormality) [SNOMED CT concept]
- Ewing's tumor [MedDRA LLT]
- Granular cell tumor (disorder) [SNOMED CT concept]
- Inclusion body fibromatosis [ICD-11 More detail]
- Inclusion body fibromatosis [HPO term]
- Juvenile aponeurotic fibroma (morphologic abnormality) [SNOMED CT concept]
- Klatskin Tumor [MeSH Descriptor]
- Klatskin's tumor (disorder) [SNOMED CT concept]
- Klatskin's tumor (morphologic abnormality) [SNOMED CT concept]
- Nephroblastoma [HPO term]
- Pancoast's tumor [MedDRA LLT]
- Pancoast's tumour [MedDRA Preferred Term]
- Papillary intralymphatic angioendothelioma of childhood (disorder) [SNOMED CT concept]
- Small cell sarcoma (morphologic abnormality) [SNOMED CT concept]
- Trichoepithelioma (disorder) [SNOMED CT concept]
- Trichoepithelioma (morphologic abnormality) [SNOMED CT concept]
- Ungual fibroma [HPO term]
- Warthin's tumor [MedDRA LLT]
- abrikosov's tumor [MeSH concept]
- abrikosov's tumor [MeSH Supplementary Concept]
- burkitt lymphoma [MeSH Descriptor]
- digital fibromatosis [SNOMED Notion]
- klatskin's tumor [SNOMED Notion]
- krukenberg tumor [MeSH Descriptor]
- sarcoma, ewing [MeSH Descriptor]
- wilms tumor [MeSH Descriptor]
Currated CISMeF NLP mapping
- Infantile digital fibromatosis [ORDO Disease]
- Infantile digital fibromatosis (disorder) [SNOMED CT concept]
- infantile digital fibromatosis [Disease (Nov.)]
Disease excludes abnormal cell
- Malignant Cell [NCIt concept]
Disease excludes normal cell origin
- Neuron, Neuroepithelial Cell, and Supporting Cell of the Nervous System [NCIt concept]
Excludes anatomical site(s)
- Bone [NCIt concept]
Has associated anatomic sites
- Connective and Soft Tissue [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Inclusion body fibromatosis [HPO term]
- Infantile digital fibromatosis [ORDO Disease]
- Infantile digital fibromatosis (disorder) [SNOMED CT concept]
- digital fibromatosis [SNOMED Notion]
- infantile digital fibromatosis [Disease (Nov.)]
disease_excludes_finding
- Locally Aggressive Lesion [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
- Well-Circumscribed Lesion [NCIt concept]
disease_has_abnormal_cell
- Neoplastic Cell [NCIt concept]
- Neoplastic Connective and Soft Tissue Cell [NCIt concept]
- Neoplastic Fibroblast [NCIt concept]
disease_has_finding
- Benign Cellular Infiltrate [NCIt concept]
- Childhood Lesion [NCIt concept]
- Indolent Clinical Course [NCIt concept]
- Infiltrative Growth Pattern [NCIt concept]
- Intracytoplasmic Eosinophilic Spherical Inclusion [NCIt concept]
disease_has_normal_cell_origin
- Connective and Soft Tissue Cell [NCIt concept]
- Fibroblast [NCIt concept]
disease_has_normal_tissue_origin
- Connective and Soft Tissue [NCIt concept]
- Soft Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Digit [NCIt concept]

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