Inclusion Body Fibromatosis

Preferred Label : Inclusion Body Fibromatosis;

NCIt synonyms : Reye's Tumor; Digital Fibrous Tumor of Reye; Reye Tumor; Infantile Digital Fibromatosis; Infantile Digital Fibroma/Fibromatosis;

NCIt definition : A benign myofibroblastic neoplasm that affects young children and is characterized by the presence of neoplastic spindle cells and intracytoplasmic eosinophilic spherical inclusions. It arises from the soft tissues of the digits or extradigital areas including the extremities, breasts, and tongue.;

Neoplastic status : Benign;

Details

Origin ID

C3456;

UMLS CUI

C1318562;

Automatic exact mappings (from CISMeF team)
- Adenolymphoma (disorder) [SNOMED CT concept]
- Adenolymphoma (morphologic abnormality) [SNOMED CT concept]
- Askin tumor (morphologic abnormality) [SNOMED CT concept]
- Askin's tumor [MedDRA LLT]
- B-cell type acute leukaemia [MedDRA Preferred Term]
- Burkitt lymphoma (morphologic abnormality) [SNOMED CT concept]
- Burkitt's lymphoma (disorder) [SNOMED CT concept]
- Burkitt's tumor [MedDRA LLT]
- Castleman Disease [MeSH Descriptor]
- Chondroblastoma (morphologic abnormality) [SNOMED CT concept]
- Eccrine dermal cylindroma of skin (disorder) [SNOMED CT concept]
- Ewing's sarcoma [MedDRA Preferred Term]
- Ewing's sarcoma (morphologic abnormality) [SNOMED CT concept]
- Ewing's tumor [MedDRA LLT]
- Granular cell tumor (disorder) [SNOMED CT concept]
- Inclusion body fibromatosis [ICD-11 More detail]
- Inclusion body fibromatosis [HPO term]
- Juvenile aponeurotic fibroma (morphologic abnormality) [SNOMED CT concept]
- Klatskin Tumor [MeSH Descriptor]
- Klatskin's tumor (disorder) [SNOMED CT concept]
- Klatskin's tumor (morphologic abnormality) [SNOMED CT concept]
- Nephroblastoma [HPO term]
- Pancoast's tumor [MedDRA LLT]
- Pancoast's tumour [MedDRA Preferred Term]
- Papillary intralymphatic angioendothelioma of childhood (disorder) [SNOMED CT concept]
- Small cell sarcoma (morphologic abnormality) [SNOMED CT concept]
- Trichoepithelioma (disorder) [SNOMED CT concept]
- Trichoepithelioma (morphologic abnormality) [SNOMED CT concept]
- Ungual fibroma [HPO term]
- Warthin's tumor [MedDRA LLT]
- abrikosov's tumor [MeSH concept]
- abrikosov's tumor [MeSH Supplementary Concept]
- burkitt lymphoma [MeSH Descriptor]
- digital fibromatosis [SNOMED Notion]
- klatskin's tumor [SNOMED Notion]
- krukenberg tumor [MeSH Descriptor]
- sarcoma, ewing [MeSH Descriptor]
- wilms tumor [MeSH Descriptor]
Currated CISMeF NLP mapping
- Infantile digital fibromatosis [ORDO Disease]
- Infantile digital fibromatosis (disorder) [SNOMED CT concept]
- infantile digital fibromatosis [Disease (Nov.)]
Disease excludes abnormal cell
- Malignant Cell [NCIt concept]
Disease excludes normal cell origin
- Neuron, Neuroepithelial Cell, and Supporting Cell of the Nervous System [NCIt concept]
Excludes anatomical site(s)
- Bone [NCIt concept]
Has associated anatomic sites
- Connective and Soft Tissue [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Inclusion body fibromatosis [HPO term]
- Infantile digital fibromatosis [ORDO Disease]
- Infantile digital fibromatosis (disorder) [SNOMED CT concept]
- digital fibromatosis [SNOMED Notion]
- infantile digital fibromatosis [Disease (Nov.)]
disease_excludes_finding
- Locally Aggressive Lesion [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
- Well-Circumscribed Lesion [NCIt concept]
disease_has_abnormal_cell
- Neoplastic Cell [NCIt concept]
- Neoplastic Connective and Soft Tissue Cell [NCIt concept]
- Neoplastic Fibroblast [NCIt concept]
disease_has_finding
- Benign Cellular Infiltrate [NCIt concept]
- Childhood Lesion [NCIt concept]
- Indolent Clinical Course [NCIt concept]
- Infiltrative Growth Pattern [NCIt concept]
- Intracytoplasmic Eosinophilic Spherical Inclusion [NCIt concept]
disease_has_normal_cell_origin
- Connective and Soft Tissue Cell [NCIt concept]
- Fibroblast [NCIt concept]
disease_has_normal_tissue_origin
- Connective and Soft Tissue [NCIt concept]
- Soft Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Digit [NCIt concept]

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