Urticaria Pigmentosa/Maculopapular Cutaneous Mastocytosis

Preferred Label : Urticaria Pigmentosa/Maculopapular Cutaneous Mastocytosis;

NCIt synonyms : Urticaria Pigmentosa; UP/MPCM; Urticaria Pigmentosa Maculopapular Cutaneous Mastocytosis;

NCIt definition : The most frequent form of cutaneous mastocytosis. In children, the lesions tend to be papular, and are characterized by aggregates of elongated or spindle-shaped mast cells which fill the papillary dermis and extend into the reticular dermis. In adults, the lesions tend to have fewer mast cells compared to those in children. The lesions are located most commonly on the trunk, but they can be seen on the extremities, head and neck. (WHO, 2001);

Neoplastic status : Undetermined;

ICD-O code : 9740/1;

Details

Origin ID

C3433;

UMLS CUI

C0042111;

Automatic exact mappings (from CISMeF team)
- Bullous cutaneous mastocytosis (disorder) [SNOMED CT concept]
- Mastocytosis, cutaneous [OMIM Phenotype]
- Urticaria pigmentosa (morphologic abnormality) [SNOMED CT concept]
Currated CISMeF NLP mapping
- Maculopapular cutaneous mastocytosis [ORDO Disease]
- Urticaria pigmentosa [PASCAL descriptor]
- Urticaria pigmentosa [ICD-11 Sub-sub category]
- Urticaria pigmentosa [ICD-11 Extension code]
- Urticaria pigmentosa [MedDRA Preferred Term]
- Urticaria pigmentosa (disorder) [SNOMED CT concept]
- urticaria pigmentosa [DO Concept]
- urticaria pigmentosa [Disease (Nov.)]
- urticaria pigmentosa [MeSH Descriptor]
- urticaria pigmentosa [MeSH concept]
- urticaria pigmentosa, nos [SNOMED Notion]
DO Cross reference
- urticaria pigmentosa [DO Concept]
Disease may have findings
- Complete Regression [NCIt concept]
- Macular Lesion [NCIt concept]
- Papular Lesion [NCIt concept]
Has associated anatomic sites
- Hematopoietic and Lymphatic System [NCIt concept]
- Integumentary System [NCIt concept]
- Skin [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Maculopapular cutaneous mastocytosis [ORDO Disease]
- Urticaria pigmentosa [ICD-11 Sub-sub category]
- Urticaria pigmentosa [MedDRA Preferred Term]
- Urticaria pigmentosa (disorder) [SNOMED CT concept]
- Urticaria pigmentosa (morphologic abnormality) [SNOMED CT concept]
- urticaria pigmentosa [DO Concept]
- urticaria pigmentosa [Disease (Nov.)]
- urticaria pigmentosa [MeSH concept]
- urticaria pigmentosa [MeSH Descriptor]
- urticaria pigmentosa, nos [SNOMED Notion]
concept_is_in_subset
- CTRP Disease Terminology [NCIt concept]
- CTRP Terminology [NCIt concept]
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
disease_excludes_finding
- Extracutaneous Dissemination of Disease [NCIt concept]
disease_has_abnormal_cell
- Neoplastic Cell [NCIt concept]
- Neoplastic Hematopoietic and Lymphoid Cell [NCIt concept]
- Neoplastic Mast Cell [NCIt concept]
- Neoplastic Myeloid Cell [NCIt concept]
disease_has_finding
- Cutaneous Involvement [NCIt concept]
- Favorable Clinical Outcome [NCIt concept]
- Monoclonal Cellular Population Present [NCIt concept]
- Rare Lesion [NCIt concept]
disease_has_normal_cell_origin
- Bone Marrow Stem Cell [NCIt concept]
- Hematopoietic and Lymphoid Cell [NCIt concept]
- Mast Cell [NCIt concept]
disease_has_normal_tissue_origin
- Hematopoietic Tissue [NCIt concept]
- Hematopoietic and Lymphoid Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Hematopoietic and Lymphatic System [NCIt concept]
- Skin [NCIt concept]
disease_may_have_associated_disease
- Telangiectasia [NCIt concept]

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