Paraganglioma - CISMeF

Preferred Label : Paraganglioma;

NCIt synonyms : Paraganglionic Tumor; Neoplasm of Paraganglion; Tumor of the Paraganglion; Paraganglionic Neoplasm; Paraganglion Neoplasm; Tumor of Paraganglion; Paraganglion Tumor; Neoplasm of the Paraganglion;

NCIt related terms : Paraganglioma, NOS;

NCIt definition : A neoplasm arising from paraganglia located along the sympathetic or parasympathetic nerves. Infrequently, it may arise outside the usual distribution of the sympathetic and parasympathetic paraganglia. Tumors arising from the adrenal gland medulla are called pheochromocytomas. Morphologically, paragangliomas usually display a nesting (Zellballen) growth pattern. There are no reliable morphologic criteria to distinguish between benign and malignant paragangliomas. The only definitive indicator of malignancy is the presence of regional or distant metastases.;

Alternative definition : NCI-GLOSS: A rare, usually benign tumor that develops from cells of the paraganglia. Paraganglia are a collection of cells that came from embryonic nervous tissue, and are found near the adrenal glands and some blood vessels and nerves. Paragangliomas that develop in the adrenal gland are called pheochromocytomas. Those that develop outside of the adrenal glands near blood vessels or nerves are called glomus tumors or chemodectomas.;

Neoplastic status : Undetermined;

ICD-O code : 8680/1;

Codes from synonyms : CDR0000390305;

Details

Origin ID

C3308;

UMLS CUI

C0030421;

Automatic exact mappings (from CISMeF team)
- Neoplasm of paraganglion [ICD-11 More detail]
- Paraganglioma NOS [ICD-9 code]
- Paraganglioma, NOS [ICD-11 Extension code]
- Paragangliomas [OMIM phenotypic series]
- Paragangliomas 1 [OMIM Phenotype]
- Paraganglion neoplasm benign [MedDRA Preferred Term]
- Paraganglionic neoplasm [ACR pathology]
Currated CISMeF NLP mapping
- Paraganglioma [PASCAL descriptor]
- Paraganglioma [HPO term]
- Paraganglioma [MedDRA LLT]
- Paraganglioma (disorder) [SNOMED CT concept]
- Paraganglioma (morphologic abnormality) [SNOMED CT concept]
- Paraganglioma, NOS [ICD-O code]
- Paraganglion neoplasm [MedDRA Preferred Term]
- paraganglioma [DO Concept]
- paraganglioma [Disease (Nov.)]
- paraganglioma [MeSH Descriptor]
- paraganglioma [MeSH concept]
- paraganglioma [Radlex concept]
- paraganglioma, nos [SNOMED Notion]
DO Cross reference
- paraganglioma [DO Concept]
Disease excludes abnormal cell
- Large Osteoclastic Giant Cell [NCIt concept]
- Neoplastic Smooth Muscle Cell [NCIt concept]
False automatic mappings
- Neoplasm of paraganglion (disorder) [SNOMED CT concept]
- Paraganglion neoplasm NOS [MedDRA LLT]
HPO term
- Paraganglioma [HPO term]
- Retroperitoneal chemodectomas [HPO term]
Has associated anatomic sites
- Nervous System [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Gangliocytic paraganglioma (disorder) [SNOMED CT concept]
- Gangliocytic paraganglioma (morphologic abnormality) [SNOMED CT concept]
- Neoplasm of paraganglion (disorder) [SNOMED CT concept]
- Paraganglioma [MedDRA LLT]
- Paraganglioma [HPO term]
- Paraganglioma [PASCAL descriptor]
- Paraganglioma (disorder) [SNOMED CT concept]
- Paraganglioma (morphologic abnormality) [SNOMED CT concept]
- Paraganglioma, NOS [ICD-O code]
- Paragangliomas 1 [OMIM Phenotype]
- Paraganglion neoplasm [MedDRA Preferred Term]
- Paraganglion neoplasm NOS [MedDRA LLT]
- gangliocytic paraganglioma [SNOMED Notion]
- paraganglioma [Radlex concept]
- paraganglioma [DO Concept]
- paraganglioma [Disease (Nov.)]
- paraganglioma [MeSH concept]
- paraganglioma [MeSH Descriptor]
- paraganglioma, nos [SNOMED Notion]
concept_is_in_subset
- CTRP Disease Terminology [NCIt concept]
- CTRP Terminology [NCIt concept]
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology Terminology [NCIt concept]
- Mapped ICDO3.1 Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology Terminology [NCIt concept]
- Mapped ICDO3.2 Terminology [NCIt concept]
- NCIt Neoplasm Core Terminology [NCIt concept]
disease_has_abnormal_cell
- Neoplastic Cell [NCIt concept]
- Neoplastic Endocrine Cell [NCIt concept]
- Neoplastic Epithelial Cell [NCIt concept]
- Neoplastic Neuroendocrine Cell [NCIt concept]
disease_has_associated_disease
- Hereditary Paraganglioma-Pheochromocytoma Syndrome [NCIt concept]
disease_has_finding
- Endocrine Differentiation [NCIt concept]
- Epithelial Component Present [NCIt concept]
- Neuroendocrine Differentiation [NCIt concept]
disease_has_normal_cell_origin
- Epithelial Cell [NCIt concept]
- Neural Crest-Derived Cell [NCIt concept]
disease_has_normal_tissue_origin
- Epithelial Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Autonomic Nervous System [NCIt concept]
- Peripheral Nerve [NCIt concept]
may_be_associated_disease_of_disease
- Multiple Endocrine Neoplasia Type 5 [NCIt concept]
- Succinate Dehydrogenase-Deficient Tumor Syndrome [NCIt concept]

Keyword's position in hierarchy(ies) :

You can consult :

recommendations
documents concerning education
documents for patients