Lymphangioleiomyoma

Preferred Label : Lymphangioleiomyoma;

NCIt synonyms : Lymphangiomyoma;

NCIt definition : A neoplasm with perivascular epithelioid cell differentiation, often associated with tuberous sclerosis. It is characterized by the presence of smooth muscle and epithelioid cells and by the proliferation of lymphatic vessels. Sites of involvement include the lymph nodes, lung, mediastinum, and retroperitoneum.;

Neoplastic status : Undetermined;

ICD-O code : 9174/0;

Details

Origin ID

C3204;

UMLS CUI

C0024223;

Automatic exact mappings (from CISMeF team)
- Lymphangiomyoma [ICD-9 code]
- Lymphangiomyoma [ICD-11 Extension code]
Currated CISMeF NLP mapping
- Lymphangiomyoma [ICD-O code]
- Lymphangiomyoma (morphologic abnormality) [SNOMED CT concept]
- lymphangiomyoma [Disease (Nov.)]
- lymphangiomyoma [MeSH Descriptor]
- lymphangiomyoma [MeSH concept]
- lymphangiomyoma [SNOMED Notion]
Excludes anatomical site(s)
- Bone [NCIt concept]
Has associated anatomic sites
- Connective and Soft Tissue [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Lymphangiomyoma [ICD-O code]
- Lymphangiomyoma (morphologic abnormality) [SNOMED CT concept]
- lymphangiomyoma [Disease (Nov.)]
- lymphangiomyoma [MeSH concept]
- lymphangiomyoma [MeSH Descriptor]
- lymphangiomyoma [SNOMED Notion]
concept_is_in_subset
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology Terminology [NCIt concept]
- Mapped ICDO3.1 Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology Terminology [NCIt concept]
- Mapped ICDO3.2 Terminology [NCIt concept]
disease_has_abnormal_cell
- Neoplastic Cell [NCIt concept]
- Neoplastic Perivascular Epithelioid Cell [NCIt concept]
disease_has_finding
- HMB-45-Positive Neoplastic Cells Present [NCIt concept]
- Perivascular Arrangement of Tumor Cells [NCIt concept]
- S-100-Positive Neoplastic Cells Present [NCIt concept]
- Smooth Muscle Component Present [NCIt concept]
- Tissue Differentiation Uncertain [NCIt concept]
disease_has_normal_tissue_origin
- Soft Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Lymphatic Vessel [NCIt concept]
disease_mapped_to_gene
- TSC2 Gene [NCIt concept]
disease_may_have_abnormal_cell
- Neoplastic Spindle Cell [NCIt concept]
disease_may_have_associated_disease
- Tuberous Sclerosis [NCIt concept]
disease_may_have_molecular_abnormality
- TSC2 Gene Mutation [NCIt concept]

Keyword's position in hierarchy(ies) :

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