Retiform Hemangioendothelioma

Preferred Label : Retiform Hemangioendothelioma;

NCIt synonyms : Hobnail Hemangioendothelioma; RHE;

NCIt definition : A rare, intermediate, locally aggressive and rarely metastasizing blood vessel neoplasm of the skin and subcutaneous tissue that usually affects the distal extremities, most often the leg. It manifests as a slow-growing red/bluish nodule or plaque and is characterized by the presence of hobnail endothelial cells and formation of arborizing vascular channels.;

Neoplastic status : Undetermined;

Details

Origin ID

C27511;

UMLS CUI

C1304512;

Currated CISMeF NLP mapping
- Retiform hemangioendothelioma (disorder) [SNOMED CT concept]
Disease excludes normal cell origin
- Epithelial Cell [NCIt concept]
Disease may have findings
- Skin Nodule [NCIt concept]
- Skin Plaque [NCIt concept]
Excludes anatomical site(s)
- Bone [NCIt concept]
Has associated anatomic sites
- Cardiovascular System [NCIt concept]
- Connective and Soft Tissue [NCIt concept]
- Integumentary System [NCIt concept]
- Skin [NCIt concept]
- Vascular System [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Retiform hemangioendothelioma (disorder) [SNOMED CT concept]
- Retiform hemangioendothelioma (morphologic abnormality) [SNOMED CT concept]
concept_is_in_subset
- NCIt Neoplasm Core Terminology [NCIt concept]
disease_excludes_finding
- High Grade Lesion [NCIt concept]
disease_excludes_normal_tissue_origin
- Epithelial Tissue [NCIt concept]
disease_has_abnormal_cell
- Neoplastic Cell [NCIt concept]
- Neoplastic Endothelial Cell [NCIt concept]
- Neoplastic Plump Endothelial Cell [NCIt concept]
disease_has_finding
- Arborizing Vascular Channel Formation [NCIt concept]
- Cutaneous Involvement [NCIt concept]
- Locally Aggressive Lesion [NCIt concept]
- Rarely Metastasizing Lesion [NCIt concept]
- Vascular Channel Formation [NCIt concept]
disease_has_normal_cell_origin
- Endothelial Cell [NCIt concept]
disease_has_normal_tissue_origin
- Blood Vessel Endothelium [NCIt concept]
- Soft Tissue [NCIt concept]
- Vascular Endothelium [NCIt concept]
disease_has_primary_anatomic_site
- Blood Vessel [NCIt concept]
- Dermis [NCIt concept]
- Skin [NCIt concept]
- Vascular System [NCIt concept]

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