Distal-Type Epithelioid Sarcoma

Preferred Label : Distal-Type Epithelioid Sarcoma;

NCIt synonyms : Conventional Epithelioid Sarcoma; Peripheral Epithelioid Sarcoma; Classic Epithelioid Sarcoma; Distal Epithelioid Sarcoma;

NCIt definition : An epithelioid sarcoma involving the extremities. It usually presents as nodular masses in the dermis and subcutaneous tissues or in the tendons and fascia. It frequently recurs and metastasizes to other anatomic sites. The most common sites of metastasis are the lungs, lymph nodes, bones, and brain.;

Neoplastic status : Malignant;

Details

Origin ID

C27473;

UMLS CUI

C1333306;

Automatic exact mappings (from CISMeF team)
- peripheral epithelioid sarcoma [DO Concept]
DO Cross reference
- peripheral epithelioid sarcoma [DO Concept]
Disease excludes normal cell origin
- Epithelial Cell [NCIt concept]
Disease may have findings
- Aggressive Clinical Course [NCIt concept]
- Loss of INI 1 Protein Expression [NCIt concept]
- Necrotic Change [NCIt concept]
- Pseudogranulomatous Pattern [NCIt concept]
Excludes anatomical site(s)
- Bone [NCIt concept]
Has associated anatomic sites
- Connective and Soft Tissue [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- peripheral epithelioid sarcoma [DO Concept]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
- Indolent Clinical Course [NCIt concept]
- Intermediate Filaments Present [NCIt concept]
- Intracytoplasmic Eosinophilic Inclusion [NCIt concept]
- Severe Cytologic Atypia [NCIt concept]
disease_excludes_normal_tissue_origin
- Epithelial Tissue [NCIt concept]
disease_has_abnormal_cell
- Malignant Cell [NCIt concept]
- Malignant Epithelioid Cell [NCIt concept]
- Malignant Spindle-Shaped to Round Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
disease_has_finding
- Malignant Cellular Infiltrate [NCIt concept]
- Metastatic/Recurrent Disease [NCIt concept]
- Nodular Pattern [NCIt concept]
- Tissue Differentiation Uncertain [NCIt concept]
disease_has_normal_tissue_origin
- Connective and Soft Tissue [NCIt concept]
- Soft Tissue [NCIt concept]
disease_may_have_cytogenetic_abnormality
- Gain of Chromosome 11q13 [NCIt concept]
- Loss of Chromosome 22q [NCIt concept]
- Loss of Chromosome 8p [NCIt concept]
- i(8)(q10) [NCIt concept]

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