Cranial Nodular Fasciitis

Preferred Label : Cranial Nodular Fasciitis;

NCIt synonyms : Cranial Pseudosarcomatous Fasciitis;

NCIt definition : A rare, self-limiting, rapidly growing, non-encapsulated benign osteolytic neoplasm that arises from the cranium. It is characterized by the presence of plump spindle-shaped fibroblasts, multinucleated osteoclast-like giant cells, chronic inflammatory infiltrate, red blood cell extravasation, and high mitotic activity.;

Neoplastic status : Benign;

Details

Origin ID

C27248;

UMLS CUI

C1333162;

Automatic exact mappings (from CISMeF team)
- cranial pseudosarcomatous fasciitis [DO Concept]
DO Cross reference
- cranial pseudosarcomatous fasciitis [DO Concept]
Disease excludes abnormal cell
- Malignant Cell [NCIt concept]
Disease excludes normal cell origin
- Neuron, Neuroepithelial Cell, and Supporting Cell of the Nervous System [NCIt concept]
Disease may have findings
- Chronic Inflammatory Infiltrate [NCIt concept]
- High Mitotic Activity [NCIt concept]
- Pain [NCIt concept]
- Red Blood Cells Extravasation [NCIt concept]
- Storiform Growth Pattern [NCIt concept]
Excludes anatomical site(s)
- Bone [NCIt concept]
- Maxillofacial Bone [NCIt concept]
Has associated anatomic sites
- Connective and Soft Tissue [NCIt concept]
- Head and Neck [NCIt concept]
- Skull [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- cranial pseudosarcomatous fasciitis [DO Concept]
disease_excludes_finding
- Encapsulated Mass [NCIt concept]
- Locally Aggressive Lesion [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
disease_has_abnormal_cell
- Neoplastic Cell [NCIt concept]
- Neoplastic Connective and Soft Tissue Cell [NCIt concept]
- Neoplastic Fibroblast [NCIt concept]
disease_has_finding
- Benign Cellular Infiltrate [NCIt concept]
- Indolent Clinical Course [NCIt concept]
- Lytic Bone Lesion [NCIt concept]
- Rapidly Enlarging Mass [NCIt concept]
disease_has_normal_cell_origin
- Connective and Soft Tissue Cell [NCIt concept]
- Fibroblast [NCIt concept]
disease_has_normal_tissue_origin
- Connective and Soft Tissue [NCIt concept]
- Soft Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Head and Neck [NCIt concept]
disease_mapped_to_gene
- MYH9/USP6 Fusion Gene [NCIt concept]
- USP6 Gene [NCIt concept]
disease_may_have_abnormal_cell
- Osteoclast-Like Giant Cell [NCIt concept]
disease_may_have_molecular_abnormality
- USP6 Gene Rearrangement [NCIt concept]

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