Preferred Label : Paroxysmal Familial Ventricular Fibrillation-2;
NCIt synonyms : VF2;
NCIt definition : An autosomal dominant condition caused by mutation(s) in the DPP6 gene, encoding A-type
potassium channel modulatory protein DPP6. It is characterized by paroxysms of ventricular
fibrillation despite the absence of any structural cardiac anomalies.;
Origin ID : C217089;
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