" /> Inborn Error of Immunity-Associated Cutaneous T-Cell Lymphoproliferative Disorder - CISMeF





Preferred Label : Inborn Error of Immunity-Associated Cutaneous T-Cell Lymphoproliferative Disorder;

NCIt synonyms : Inborn Error of Immunity-Associated T Lymphoproliferative Disorder; Granulomatous CD8-Positive T-Cell Lymphoproliferative Disorder; CD8-Positive Granulomatous Cutaneous T-Cell Lymphoma; Inborn Error of Immunity-Associated T-Cell Lymphoproliferative Disorder; IEI-Associated T LPD;

NCIt definition : A cutaneous EBV-negative lymphoproliferative disorder that is composed of CD8-positive T-cells and is associated with inborn immunodeficiency. The cutaneous manifestations include generalized papulo-nodular indurated lesions. It infrequently affects the subcutaneous tissue, lungs, bone marrow, and gastrointestinal tract as well. It has a variable clinical course.;

Neoplastic status : Undetermined;

NCI Metathesaurus CUI : CL1928925;

Details


Keyword's position in hierarchy(ies) : arborescence

You can consult :


Nous contacter.
04/05/2025


[Home] [Top]

© Rouen University Hospital. Any partial or total use of this material must mention the source.