Cutaneous Blastic Plasmacytoid Dendritic Cell Neoplasm

Preferred Label : Cutaneous Blastic Plasmacytoid Dendritic Cell Neoplasm;

NCIt synonyms : Skin Blastic Plasmacytoid Dendritic Cell Neoplasm;

NCIt definition : A blastic plasmacytoid dendritic cell neoplasm that affects the skin. It manifests with patches, plaques, and nodules.;

Neoplastic status : Malignant;

NCI Metathesaurus CUI : CL1928558;

Details

Origin ID

C206208;

Disease may have findings
- Aggressive Clinical Course [NCIt concept]
- Lymphadenopathy [NCIt concept]
- Widespread Disease [NCIt concept]
Has associated anatomic sites
- Hematopoietic and Lymphatic System [NCIt concept]
- Integumentary System [NCIt concept]
- Skin [NCIt concept]
disease_excludes_finding
- CD30-Positive Neoplastic Cells Present [NCIt concept]
- HMB-45-Positive Neoplastic Cells Present [NCIt concept]
disease_excludes_molecular_abnormality
- Clonal Immunoglobulin Gene Rearrangement [NCIt concept]
- Clonal T-Cell Receptor Gene Rearrangement [NCIt concept]
disease_has_abnormal_cell
- CD4+/CD56+ Neoplastic Medium-Sized Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Hematopoietic and Lymphoid Cell [NCIt concept]
- Neoplastic Histiocytic and Dendritic Cell [NCIt concept]
disease_has_finding
- CD4-Positive Neoplastic Cells Present [NCIt concept]
- CD56-Positive Neoplastic Cells Present [NCIt concept]
- Cutaneous Involvement [NCIt concept]
- Histiocytosis [NCIt concept]
- Rare Lesion [NCIt concept]
- Skin Nodule [NCIt concept]
disease_has_normal_cell_origin
- Hematopoietic and Lymphoid Cell [NCIt concept]
- Histiocyte [NCIt concept]
- Histiocytic and Dendritic Cell [NCIt concept]
- Plasmacytoid Dendritic Cell [NCIt concept]
disease_has_normal_tissue_origin
- Hematopoietic and Lymphoid Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Hematopoietic and Lymphatic System [NCIt concept]

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