Head and Neck Juvenile Xanthogranuloma

Preferred Label : Head and Neck Juvenile Xanthogranuloma;

NCIt definition : A benign histiocytic tumor that usually arises from the skin of the head and neck and occurs during childhood. It is distinct from Langerhans cell histiocytosis. Rarely, it can arise from extracutaneous head and neck sites, including the eye, ocular adnexa, oral cavity, paranasal sinuses, and ear. It is characterized by the presence of lipid-laden, foamy histiocytes and Touton-type giant cells.;

Neoplastic status : Benign;

Details

Origin ID

C202967;

Disease excludes abnormal cell
- Malignant Cell [NCIt concept]
Has associated anatomic sites
- Head and Neck [NCIt concept]
- Hematopoietic and Lymphatic System [NCIt concept]
disease_excludes_finding
- CD30-Positive Neoplastic Cells Present [NCIt concept]
- HMB-45-Positive Neoplastic Cells Present [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
disease_excludes_molecular_abnormality
- Clonal Immunoglobulin Gene Rearrangement [NCIt concept]
- Clonal T-Cell Receptor Gene Rearrangement [NCIt concept]
disease_has_abnormal_cell
- Lipid-Laden Macrophage [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Hematopoietic and Lymphoid Cell [NCIt concept]
- Neoplastic Histiocytic and Dendritic Cell [NCIt concept]
- Touton Giant Cell [NCIt concept]
disease_has_finding
- Benign Cellular Infiltrate [NCIt concept]
- Histiocytosis [NCIt concept]
- Juvenile Lesion [NCIt concept]
- Rare Lesion [NCIt concept]
disease_has_normal_cell_origin
- Hematopoietic and Lymphoid Cell [NCIt concept]
- Histiocyte [NCIt concept]
- Histiocytic and Dendritic Cell [NCIt concept]
disease_has_normal_tissue_origin
- Hematopoietic and Lymphoid Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Head and Neck [NCIt concept]
- Hematopoietic and Lymphatic System [NCIt concept]
disease_may_have_associated_disease
- Neurofibromatosis Type 1 [NCIt concept]

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