Cutaneous Juvenile Xanthogranuloma

Preferred Label : Cutaneous Juvenile Xanthogranuloma;

NCIt definition : A benign histiocytic tumor that arises from the skin and occurs during childhood; it is distinct from Langerhans cell histiocytosis. It is characterized by the presence of lipid-laden, foamy histiocytes and Touton-type giant cells in the dermis. The lesions usually develop during infancy. They consist of cutaneous papules and nodules (most often in the head and neck).;

Neoplastic status : Benign;

NCI Metathesaurus CUI : CL1922102;

Détails

Origin ID

C202966;

UMLS CUI

C5908876;

Disease excludes abnormal cell
- Malignant Cell [NCIt concept]
Disease may have findings
- Nodular Lesion [NCIt concept]
- Papular Lesion [NCIt concept]
Has associated anatomic sites
- Hematopoietic and Lymphatic System [NCIt concept]
- Integumentary System [NCIt concept]
- Skin [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
disease_excludes_finding
- CD30-Positive Neoplastic Cells Present [NCIt concept]
- Dysplasia [NCIt concept]
- HMB-45-Positive Neoplastic Cells Present [NCIt concept]
- Invasive Lesion [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
disease_excludes_molecular_abnormality
- Clonal Immunoglobulin Gene Rearrangement [NCIt concept]
- Clonal T-Cell Receptor Gene Rearrangement [NCIt concept]
disease_has_abnormal_cell
- Lipid-Laden Macrophage [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Hematopoietic and Lymphoid Cell [NCIt concept]
- Neoplastic Histiocytic and Dendritic Cell [NCIt concept]
- Touton Giant Cell [NCIt concept]
disease_has_finding
- Benign Cellular Infiltrate [NCIt concept]
- Cutaneous Involvement [NCIt concept]
- Histiocytosis [NCIt concept]
- Juvenile Lesion [NCIt concept]
- Rare Lesion [NCIt concept]
disease_has_normal_cell_origin
- Hematopoietic and Lymphoid Cell [NCIt concept]
- Histiocyte [NCIt concept]
- Histiocytic and Dendritic Cell [NCIt concept]
disease_has_normal_tissue_origin
- Hematopoietic and Lymphoid Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Hematopoietic and Lymphatic System [NCIt concept]
- Skin [NCIt concept]
disease_may_have_associated_disease
- Neurofibromatosis Type 1 [NCIt concept]

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