Gigantiform Cementoma

Preferred Label : Gigantiform Cementoma;

NCIt synonyms : Florid Osseous Dysplasia; Expansive Osseous Dysplasia; Familial Gigantiform Cementoma; FGC;

NCIt definition : An extremely rare, benign, rapidly progressing fibro-osseous lesion that arises from the jaws as a multifocal expansile growth in children or adolescents. It results in significant deformity, orbital distortion, and possible airway involvement. An autosomal dominant inheritance has been proposed. Histologically, it is characterized by the presence of immature bony trabeculae and cementum-like calcifications within a hypercellular fibroblastic stroma. It shares morphological features with florid cemento-osseous dysplasia, but in florid cemento-osseous dysplasia the degree of expansion is less prominent and patients are usually older.;

Détails

Origin ID

C202219;

UMLS CUI

C3495361;

Has associated anatomic sites
- Head and Neck [NCIt concept]
- Lip and Oral Cavity [NCIt concept]
- Oral Cavity [NCIt concept]
- Tooth [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Familial gigantiform cementoma [MedDRA Preferred Term]
- Gigantiform cementoma (morphologic abnormality) [SNOMED CT concept]
- Gigantiform cementoma, familial [OMIM Phenotype]
- gigantiform cementoma [SNOMED Notion]
- gigantiform cementoma, familial [MeSH Supplementary Concept]
- gigantiform cementoma, familial [MeSH concept]
concept_is_in_subset
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology Terminology [NCIt concept]
- Mapped ICDO3.1 Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology Terminology [NCIt concept]
- Mapped ICDO3.2 Terminology [NCIt concept]
disease_has_primary_anatomic_site
- Head and Neck [NCIt concept]
- Oral Cavity [NCIt concept]
- Tooth [NCIt concept]

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