NCIt definition : An extremely rare, benign, rapidly progressing fibro-osseous lesion that arises from
the jaws as a multifocal expansile growth in children or adolescents. It results in
significant deformity, orbital distortion, and possible airway involvement. An autosomal
dominant inheritance has been proposed. Histologically, it is characterized by the
presence of immature bony trabeculae and cementum-like calcifications within a hypercellular
fibroblastic stroma. It shares morphological features with florid cemento-osseous
dysplasia, but in florid cemento-osseous dysplasia the degree of expansion is less
prominent and patients are usually older.;
Has associated anatomic sites