" /> SMARCB1-Deficient Sinonasal Carcinoma - CISMeF





Preferred Label : SMARCB1-Deficient Sinonasal Carcinoma;

NCIt synonyms : Sinonasal SMARCB1-Deficient Carcinoma;

NCIt definition : An SWI/SNF-deficient sinonasal carcinoma characterized by biallelic deletion or inactivating mutation of SMARCB1 gene. It usually affects the paranasal sinuses, especially ethmoid. It is composed of a monomorphic malignant epithelial cellular population with a predominantly basaloid or plasmacytoid/rhabdoid morphology.;

Neoplastic status : Malignant;

NCI Metathesaurus CUI : CL1920827;

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24/07/2025


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