Solid Pseudopapillary Neoplasm

Preferred Label : Solid Pseudopapillary Neoplasm;

NCIt synonyms : Frantz Tumor;

NCIt related terms : Solid pseudopapillary tumor;

NCIt definition : A low-grade malignant neoplasm that arises from the exocrine pancreas. Rare cases arising from ectopic pancreatic tissue in the ovary have also been described. It is characterized by the presence of uniform cells that form solid and pseudopapillary patterns, cystic changes, and hemorrhage. It usually presents as an encapsulated, solitary, and lobulated mass. It occurs predominantly in young women. Complete removal of the tumor is curative in the majority of cases.;

Neoplastic status : Malignant;

ICD-O code : 8452/1;

Details

Origin ID

C201136;

concept_is_in_subset
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology Terminology [NCIt concept]
- Mapped ICDO3.1 Terminology [NCIt concept]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
disease_has_abnormal_cell
- Malignant Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
disease_has_finding
- Cystic Change [NCIt concept]
- Lobulated Growth Pattern [NCIt concept]
- Low Grade Lesion [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
- Pseudopapillary Pattern [NCIt concept]
disease_has_grade
- Low Grade [NCIt concept]
disease_mapped_to_gene
- CTNNB1 Gene [NCIt concept]
disease_may_have_molecular_abnormality
- CTNNB1 Gene Mutation [NCIt concept]
pathogenesis_of_disease_involves_gene
- CTNNB1 Gene [NCIt concept]
- CTNNB1 wt Allele [NCIt concept]

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