Lymphocytic Variant Hypereosinophilic Syndrome

Preferred Label : Lymphocytic Variant Hypereosinophilic Syndrome;

NCIt synonyms : LHS; LHES;

NCIt related terms : Lymphocytic Variant Hypereosinophilic Syndrome [LHES];

NCIt definition : A hypereosinophilic syndrome characterized by the presence of a clonal T-cell population. Patients present with cutaneous findings including eczematous dermatitis, nodules, papules, and pruritis, rheumatological symptoms, gastrointestinal symptoms, and lymphadenopathy. Lymph node biopsies show eosinophilia, atypical lymphocytes, clonally rearranged T-cells, and architectural distortion. Skin biopsies may also show the clonally rearranged T-cell population.;

NCI Metathesaurus CUI : CL1634320;

Codes from synonyms : D72.111;

Details

Origin ID

C197926;

UMLS CUI

C5389713;

Semantic type(s)
- Disease or Syndrome [UMLS semantic type]
concept_is_in_subset
- mCode Cancer Disorder Value Set [NCIt concept]
- mCode Primary Cancer Disorder Value Set [NCIt concept]
- mCode Specific Diagnosis of Cancer Value Set [NCIt concept]
- mCode Terminology [NCIt concept]
disease_excludes_finding
- Monoclonal Eosinophils Present [NCIt concept]
disease_has_finding
- Eosinophilia [NCIt concept]
disease_has_molecular_abnormality
- Clonal T-Cell Receptor Gene Rearrangement [NCIt concept]

Keyword's position in hierarchy(ies) :

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