NCIt definition : Human MCCC1 wild-type allele is located in the vicinity of 3q27.1 and is approximately
101 kb in length. This allele, which encodes methylcrotonoyl-CoA carboxylase subunit
alpha, mitochondrial protein, is involved in biotin binding and the metabolism of
branched-chain amino acids. Mutation of the gene is associated with 3-methylcrotonylglycinuria
caused by 3-methylcrotonyl-CoA carboxylase 1 deficiency.;