Childhood Fibrolamellar Carcinoma

Preferred Label : Childhood Fibrolamellar Carcinoma;

NCIt synonyms : Pediatric Fibrolamellar Carcinoma;

NCIt definition : A fibrolamellar variant of hepatocellular carcinoma that occurs during childhood.;

Neoplastic status : Malignant;

NCI Metathesaurus CUI : CL1798522;

Details

Origin ID

C189932;

UMLS CUI

C5708841;

Disease excludes abnormal cell
- Malignant Squamous Cell [NCIt concept]
- Malignant Stromal Cell [NCIt concept]
- Neoplastic Smooth Muscle Cell [NCIt concept]
- Neoplastic Squamous Cell [NCIt concept]
Disease excludes normal cell origin
- Embryonic Cell [NCIt concept]
Excludes anatomical site(s)
- Extrahepatic Bile Duct [NCIt concept]
- Intrahepatic Bile Duct [NCIt concept]
Has associated anatomic sites
- Digestive System [NCIt concept]
- Hepatobiliary System [NCIt concept]
- Liver [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
- Cirrhosis [NCIt concept]
- Favorable Clinical Outcome [NCIt concept]
- Intermediate Grade Neuroendocrine Lesion [NCIt concept]
- Low Grade Neuroendocrine Lesion [NCIt concept]
- Mixed Neoplastic Glandular and Squamous Cell Population [NCIt concept]
- Well Differentiated Neuroendocrine Lesion [NCIt concept]
disease_has_abnormal_cell
- Adenocarcinoma Cell [NCIt concept]
- Adenocarcinoma Cell with Eosinophilic Granular Cytoplasm [NCIt concept]
- Malignant Cell [NCIt concept]
- Malignant Epithelial Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Epithelial Cell [NCIt concept]
- Neoplastic Glandular Cell [NCIt concept]
- Polygonal Adenocarcinoma Cell with Eosinophilic Cytoplasm [NCIt concept]
disease_has_finding
- Carcinomatous Component Present [NCIt concept]
- Childhood Lesion [NCIt concept]
- Epithelial Component Present [NCIt concept]
- Lamellar Pattern [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
- Rare Lesion [NCIt concept]
disease_has_normal_cell_origin
- Epithelial Cell [NCIt concept]
- Hepatocyte [NCIt concept]
disease_has_normal_tissue_origin
- Epithelial Tissue [NCIt concept]
- Hepatic Tissue [NCIt concept]
- Hepatobiliary Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Digestive System [NCIt concept]
- Hepatobiliary System [NCIt concept]
- Liver [NCIt concept]
disease_mapped_to_gene
- DNAJB1/PRKACA Fusion Gene [NCIt concept]
disease_may_have_cytogenetic_abnormality
- Loss of Chromosome 19 [NCIt concept]
disease_may_have_molecular_abnormality
- DNAJB1-PRKACA Fusion Protein Expression [NCIt concept]
- PRKAR1A Gene Mutation [NCIt concept]

Keyword's position in hierarchy(ies) :

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