Central Nervous System Dedifferentiated Solitary Fibrous Tumor

Preferred Label : Central Nervous System Dedifferentiated Solitary Fibrous Tumor;

NCIt synonyms : CNS Anaplastic Solitary Fibrous Tumor; Central Nervous System Anaplastic Solitary Fibrous Tumor; CNS Dedifferentiated Solitary Fibrous Tumor;

NCIt definition : A central nervous system solitary fibrous tumor characterized by the presence of areas of abrupt transition to high grade sarcoma.;

Neoplastic status : Malignant;

NCI Metathesaurus CUI : CL1778781;

Details

Origin ID

C186603;

UMLS CUI

C5670656;

Disease excludes abnormal cell
- Immature Malignant Mast Cell [NCIt concept]
Disease excludes normal cell origin
- Neuron, Neuroepithelial Cell, and Supporting Cell of the Nervous System [NCIt concept]
Disease may have findings
- Increased Cellularity Present [NCIt concept]
Excludes anatomical site(s)
- Bone [NCIt concept]
- Lung [NCIt concept]
Has associated anatomic sites
- Central Nervous System [NCIt concept]
- Connective and Soft Tissue [NCIt concept]
- Nervous System [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
- Indolent Clinical Course [NCIt concept]
disease_has_abnormal_cell
- Malignant Cell [NCIt concept]
- Malignant Spindle-Shaped to Round Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Connective and Soft Tissue Cell [NCIt concept]
- Neoplastic Fibroblast [NCIt concept]
- Neoplastic Spindle-Shaped to Round Cell [NCIt concept]
disease_has_finding
- Atypia [NCIt concept]
- Dedifferentiated Lesion [NCIt concept]
- High Grade Lesion [NCIt concept]
- High Mitotic Activity [NCIt concept]
- Hyalinized Stroma Formation [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
- Necrotic Change [NCIt concept]
- Nuclear Expression of STAT6 Protein [NCIt concept]
- Thin Bands of Collagen Present [NCIt concept]
- Thin-Walled Branching Vascular Pattern [NCIt concept]
disease_has_grade
- Grade 3 [NCIt concept]
disease_has_normal_cell_origin
- Connective and Soft Tissue Cell [NCIt concept]
- Fibroblast [NCIt concept]
disease_has_normal_tissue_origin
- Connective and Soft Tissue [NCIt concept]
- Soft Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Central Nervous System [NCIt concept]
disease_mapped_to_gene
- NAB2/STAT6 Fusion Gene [NCIt concept]

Keyword's position in hierarchy(ies) :

You can consult :

recommendations
documents concerning education
documents for patients