" /> Spinal Cord Ependymoma, MYCN Amplified - CISMeF





Preferred Label : Spinal Cord Ependymoma, MYCN Amplified;

NCIt synonyms : Spinal Ependymoma, MYCN Amplified; Spinal Ependymoma, MYCN-Amplified; Spinal Cord Ependymoma, MYCN-Amplified;

NCIt definition : A rare, aggressive ependymoma that arises from the spinal cord. It displays microvascular proliferation, necrosis, and high mitotic rate. It is characterized by high-level MYCN amplification. Cytogenetic abnormalities include loss of chromosome 10 and focal losses on chromosome 11q. The prognosis is poor.;

Neoplastic status : Malignant;

NCI Metathesaurus CUI : CL1778904;

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30/07/2025


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