Vulvar Distal-Type Epithelioid Sarcoma

Preferred Label : Vulvar Distal-Type Epithelioid Sarcoma;

NCIt definition : A rare epithelioid sarcoma of the distal type that arises from the vulva.;

Neoplastic status : Malignant;

NCI Metathesaurus CUI : CL1664907;

Details

Origin ID

C181973;

UMLS CUI

C5557400;

Disease excludes normal cell origin
- Epithelial Cell [NCIt concept]
Disease may have findings
- Aggressive Clinical Course [NCIt concept]
- Loss of INI 1 Protein Expression [NCIt concept]
- Necrotic Change [NCIt concept]
- Pseudogranulomatous Pattern [NCIt concept]
Excludes anatomical site(s)
- Bone [NCIt concept]
Has associated anatomic sites
- Connective and Soft Tissue [NCIt concept]
- Female Reproductive System [NCIt concept]
- Genitourinary System [NCIt concept]
- Reproductive System [NCIt concept]
- Vulva [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
- Indolent Clinical Course [NCIt concept]
- Intermediate Filaments Present [NCIt concept]
- Intracytoplasmic Eosinophilic Inclusion [NCIt concept]
- Severe Cytologic Atypia [NCIt concept]
disease_excludes_normal_tissue_origin
- Epithelial Tissue [NCIt concept]
disease_has_abnormal_cell
- Malignant Cell [NCIt concept]
- Malignant Epithelioid Cell [NCIt concept]
- Malignant Spindle-Shaped to Round Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
disease_has_finding
- Malignant Cellular Infiltrate [NCIt concept]
- Metastatic/Recurrent Disease [NCIt concept]
- Nodular Pattern [NCIt concept]
- Tissue Differentiation Uncertain [NCIt concept]
disease_has_normal_tissue_origin
- Connective and Soft Tissue [NCIt concept]
- Soft Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Female Reproductive System [NCIt concept]
- Vulva [NCIt concept]
disease_may_have_cytogenetic_abnormality
- Gain of Chromosome 11q13 [NCIt concept]
- Loss of Chromosome 22q [NCIt concept]
- Loss of Chromosome 8p [NCIt concept]
- i(8)(q10) [NCIt concept]

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