Vulvar Lipoblastoma-Like Tumor

Preferred Label : Vulvar Lipoblastoma-Like Tumor;

NCIt synonyms : Vulvar Lipoblastoma-Like Neoplasm;

NCIt definition : A benign, well-defined, lobulated, myxoid or gelatinous tumor that arises from the vulva. It shares morphological features with lipoblastoma, myxoid liposarcoma, and spindle cell lipoma. It is characterized by a lobulated growth and is composed of mature adipocytes, lipoblasts, and spindle cells without atypia in a myxoid matrix. DDIT3 and PLAG1 gene rearrangements seen in lipoblastoma and myxoid liposarcoma are not present in this tumor. It can recur infrequently and there are no reports of metastasis.;

Neoplastic status : Benign;

NCI Metathesaurus CUI : CL1664943;

Details

Origin ID

C181925;

UMLS CUI

C5557368;

Disease excludes abnormal cell
- Adenocarcinoma Cell with Intracytoplasmic Mucin [NCIt concept]
- Malignant Cell [NCIt concept]
- Malignant Stromal Cell [NCIt concept]
- Serous Adenocarcinoma Cell [NCIt concept]
Disease excludes normal cell origin
- Neuron, Neuroepithelial Cell, and Supporting Cell of the Nervous System [NCIt concept]
Excludes anatomical site(s)
- Bone [NCIt concept]
Has associated anatomic sites
- Connective and Soft Tissue [NCIt concept]
- Female Reproductive System [NCIt concept]
- Genitourinary System [NCIt concept]
- Reproductive System [NCIt concept]
- Vulva [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
disease_excludes_finding
- Cytologic Atypia [NCIt concept]
- Locally Aggressive Lesion [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
disease_has_abnormal_cell
- Neoplastic Cell [NCIt concept]
- Neoplastic Connective and Soft Tissue Cell [NCIt concept]
- Neoplastic Lipoblast [NCIt concept]
- Neoplastic Lipocyte [NCIt concept]
- Neoplastic Mature Adipocyte [NCIt concept]
- Neoplastic Spindle-Shaped Adipocyte [NCIt concept]
disease_has_finding
- Benign Cellular Infiltrate [NCIt concept]
- Indolent Clinical Course [NCIt concept]
- Lobulated Growth Pattern [NCIt concept]
- Myxoid Stroma Formation [NCIt concept]
disease_has_normal_cell_origin
- Adipocyte [NCIt concept]
- Connective and Soft Tissue Cell [NCIt concept]
disease_has_normal_tissue_origin
- Adipose Tissue [NCIt concept]
- Connective and Soft Tissue [NCIt concept]
- Soft Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Female Reproductive System [NCIt concept]
- Genitourinary System [NCIt concept]
- Reproductive System [NCIt concept]
- Vulva [NCIt concept]

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