Conventional Chordoma

Preferred Label : Conventional Chordoma;

NCIt definition : A malignant bone tumor arising from the remnants of the fetal notochord. It is characterized by the presence of large epithelioid cells with clear to light eosinophilic cytoplasm. Some of the cells are large with bubbly, vacuolated cytoplasm (physaliphorous cells). The cells form cords and nests that are embedded within an extracellular myxoid matrix.;

Neoplastic status : Malignant;

NCI Metathesaurus CUI : CL1648079;

Details

Origin ID

C178563;

UMLS CUI

C5555136;

Disease excludes normal cell origin
- Bone Marrow Stem Cell [NCIt concept]
Has associated anatomic sites
- Bone [NCIt concept]
- Connective and Soft Tissue [NCIt concept]
- Musculoskeletal System [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
- Indolent Clinical Course [NCIt concept]
- Sarcomatous Component Present [NCIt concept]
disease_excludes_normal_tissue_origin
- Germinal Layer [NCIt concept]
disease_has_abnormal_cell
- Malignant Cell [NCIt concept]
- Malignant Epithelioid Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Physaliphorous Cell [NCIt concept]
disease_has_finding
- Lobulated Growth Pattern [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
- Myxoid Stroma Formation [NCIt concept]
disease_has_normal_cell_origin
- Embryonic Cell [NCIt concept]
disease_has_normal_tissue_origin
- Embryonic Tissue [NCIt concept]
- Remnants of the Notochord [NCIt concept]
disease_has_primary_anatomic_site
- Bone [NCIt concept]

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