Primitive Non-Neural Granular Cell Tumor

Preferred Label : Primitive Non-Neural Granular Cell Tumor;

NCIt synonyms : Primitive Polypoid Granular Cell Tumor; Non-Neural Granular Cell Tumor; PNNGCT; Dermal Non-Neural Granular Cell Tumor;

NCIt definition : A rare, low-grade skin neoplasm of mesenchymal cells of unknown lineage with prominent cytoplasmic granularity. The lesions are most commonly non-ulcerated papules or nodules. Most cases are indolent, despite worrisome histopathologic features. Few cases with regional lymph node metastasis have been reported. (WHO 2018);

Neoplastic status : Uncertain Malignant Potential;

NCI Metathesaurus CUI : CL978773;

Details

Origin ID

C172637;

UMLS CUI

C5230988;

Automatic exact mappings (from CISMeF team)
- Primitive non-neural granular cell tumor (morphologic abnormality) [SNOMED CT concept]
Currated CISMeF NLP mapping
- Primitive non-neural granular cell tumor [ICD-11 Extension code]
Disease excludes normal cell origin
- Epithelial Cell [NCIt concept]
Disease may have findings
- Indolent Clinical Course [NCIt concept]
- Nodular Lesion [NCIt concept]
- Papular Lesion [NCIt concept]
Excludes anatomical site(s)
- Bone [NCIt concept]
Has associated anatomic sites
- Connective and Soft Tissue [NCIt concept]
- Integumentary System [NCIt concept]
- Skin [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Primitive non-neural granular cell tumor (morphologic abnormality) [SNOMED CT concept]
disease_excludes_normal_tissue_origin
- Epithelial Tissue [NCIt concept]
disease_has_abnormal_cell
- Neoplastic Cell [NCIt concept]
disease_has_finding
- Cellular Granularity Present [NCIt concept]
- Cutaneous Involvement [NCIt concept]
- Low Grade Lesion [NCIt concept]
disease_has_grade
- Low Grade [NCIt concept]
disease_has_normal_tissue_origin
- Soft Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Skin [NCIt concept]

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