NCIt definition : A rare, low-grade sweat gland carcinoma with neuroendocrine differentiation. It usually
arises on the eyelids and periorbital skin. It affects mostly older individuals. Women
are affected more frequently than men. Morphologically, it is characterized by well-demarcated
nodules with cystic, papillary, or cribriform architectural patterns. The neoplastic
cells are small to intermediate polygonal to round cells. Small amounts of intracellular
or extracellular mucin are present. In some cases, this carcinoma is a precursor of
mucinous carcinoma.;