NCIt definition : A recurrent form of cholangitis that is characterized by intrabiliary pigment stone
formation, biliary tree stricture and obstruction, and recurrent bouts of cholangitis.
There is an association with biliary parasitosis, but evidence supporting these infections
in the pathogenesis of recurrent pyogenic cholangitis is inconclusive. The most common
causes of death are sepsis, liver failure, or complications from cirrhosis. Patients
are also at increased risk of cholangiocarcinoma.;