Refractory Hemophagocytic Lymphohistiocytosis

Preferred Label : Refractory Hemophagocytic Lymphohistiocytosis;

NCIt definition : Hemophagocytic lymphohistiocytosis that is resistant to treatment.;

NCI Metathesaurus CUI : CL554414;

Details

Origin ID

C153297;

UMLS CUI

C4727152;

Disease may have findings
- Fever [NCIt concept]
- Hepatomegaly [NCIt concept]
- Lymphadenopathy [NCIt concept]
- Pancytopenia [NCIt concept]
- Splenomegaly [NCIt concept]
Has associated anatomic sites
- Hematopoietic and Lymphatic System [NCIt concept]
Semantic type(s)
- Disease or Syndrome [UMLS semantic type]
concept_is_in_subset
- CTRP Disease Terminology [NCIt concept]
- CTRP Terminology [NCIt concept]
disease_has_abnormal_cell
- Atypical Histiocyte [NCIt concept]
disease_has_finding
- Hemophagocytosis [NCIt concept]
- Histiocytosis [NCIt concept]
- Rare Lesion [NCIt concept]
- Refractory Disease [NCIt concept]
disease_has_normal_cell_origin
- Hematopoietic and Lymphoid Cell [NCIt concept]
- Histiocyte [NCIt concept]
disease_has_normal_tissue_origin
- Hematopoietic and Lymphoid Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Hematopoietic and Lymphatic System [NCIt concept]

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