Langerhans Cell Histiocytosis, Polyostotic

Preferred Label : Langerhans Cell Histiocytosis, Polyostotic;

NCIt related terms : Langerhans cell histiocytosis, poly-ostotic;

NCIt definition : Langerhans cell histiocytosis presenting with multiple sites of involvement.;

Neoplastic status : Undetermined;

NCI Metathesaurus CUI : CL552504;

Details

Origin ID

C150702;

UMLS CUI

C4727834;

Automatic exact mappings (from CISMeF team)
- Langerhans cell histiocytosis, multifocal (morphologic abnormality) [SNOMED CT concept]
- Langerhans cell histiocytosis, polyostotic [ICD-11 Extension code]
Disease may have findings
- CD68-Positive Neoplastic Cells Present [NCIt concept]
- Sinusoidal Infiltration [NCIt concept]
Has associated anatomic sites
- Hematopoietic and Lymphatic System [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Polyostotic Langerhans cell histiocytosis (morphologic abnormality) [SNOMED CT concept]
concept_is_in_subset
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
disease_excludes_finding
- CD21-Positive Neoplastic Cells Present [NCIt concept]
- CD30-Positive Neoplastic Cells Present [NCIt concept]
- CD35-Positive Neoplastic Cells Present [NCIt concept]
- HMB-45-Positive Neoplastic Cells Present [NCIt concept]
- High Grade Lesion [NCIt concept]
disease_excludes_molecular_abnormality
- Clonal Immunoglobulin Gene Rearrangement [NCIt concept]
- Clonal T-Cell Receptor Gene Rearrangement [NCIt concept]
disease_has_abnormal_cell
- Neoplastic Cell [NCIt concept]
- Neoplastic Hematopoietic and Lymphoid Cell [NCIt concept]
- Neoplastic Histiocytic and Dendritic Cell [NCIt concept]
- Neoplastic Langerhans Cell [NCIt concept]
disease_has_finding
- Birbeck Granules Present [NCIt concept]
- CD1a-Positive Neoplastic Cells Present [NCIt concept]
- Histiocytosis [NCIt concept]
- Monoclonal Langerhans Cells Present [NCIt concept]
- Multifocal Lesion [NCIt concept]
- Polymorphic Cellular Infiltrate [NCIt concept]
- Rare Lesion [NCIt concept]
- S-100-Positive Neoplastic Cells Present [NCIt concept]
disease_has_normal_cell_origin
- Hematopoietic and Lymphoid Cell [NCIt concept]
- Histiocyte [NCIt concept]
- Histiocytic and Dendritic Cell [NCIt concept]
- Langerhans Cell [NCIt concept]
disease_has_normal_tissue_origin
- Hematopoietic and Lymphoid Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Hematopoietic and Lymphatic System [NCIt concept]
disease_may_have_molecular_abnormality
- BRAF Gene Mutation [NCIt concept]

Keyword's position in hierarchy(ies) :

You can consult :

recommendations
documents concerning education
documents for patients