NCIt definition : An EBV-positive NK-cell lymphoproliferative disorder characterized by high fever and
intense local skin symptoms, including erythema, bullae, ulcers, skin necrosis, and
deep scarring following mosquito bites. Patients have NK-cell lymphocytosis in the
peripheral blood and an increased risk of developing hemophagocytic syndrome and progressing
into overt NK/T-cell lymphoma or aggressive NK-cell leukemia in the longstanding clinical
course. (WHO 2017);