Congenital Peribronchial Myofibroblastic Tumor

Preferred Label : Congenital Peribronchial Myofibroblastic Tumor;

NCIt synonyms : Congenital Bronchopulmonary Leiomyosarcoma; Congenital Pulmonary Myofibroblastic Tumor; Congenital Fibrosarcoma; Congenital Mesenchymal Malformation of Lung; Neonatal Pulmonary Hamartoma;

NCIt definition : A rare lung neoplasm that occurs in the intrauterine and perinatal period. It is characterized by the proliferation of spindle cells in an interstitial, peribronchial pattern. Surgical resection of the involved lung parenchyma is the treatment of choice.;

Neoplastic status : Undetermined;

Details

Origin ID

C142823;

UMLS CUI

C1266124;

Automatic exact mappings (from CISMeF team)
- Congenital fibrosarcoma [MedDRA Preferred Term]
- Infantile fibrosarcoma [ICD-11 Extension code]
- Infantile fibrosarcoma (morphologic abnormality) [SNOMED CT concept]
- Myofibroblastic tumor, peribronchial (morphologic abnormality) [SNOMED CT concept]
- Myofibroblastic tumour, peribronchial [ICD-11 Extension code]
- congenital fibrosarcoma [DO Concept]
Excludes anatomical site(s)
- Bone [NCIt concept]
- Neck [NCIt concept]
Has associated anatomic sites
- Connective and Soft Tissue [NCIt concept]
- Lung [NCIt concept]
- Respiratory System [NCIt concept]
- Thoracic Cavity [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Myofibroblastic tumor, peribronchial [ICD-O code]
- Myofibroblastic tumor, peribronchial (morphologic abnormality) [SNOMED CT concept]
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- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
disease_has_abnormal_cell
- Neoplastic Cell [NCIt concept]
- Neoplastic Spindle Cell [NCIt concept]
disease_has_finding
- Childhood Lesion [NCIt concept]
- Congenital Lesion [NCIt concept]
- Peribronchial Proliferation of Neoplastic Cells Present [NCIt concept]
disease_has_normal_tissue_origin
- Soft Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Lung [NCIt concept]

Keyword's position in hierarchy(ies) :

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