" /> Primary Cutaneous Acral CD8-Positive T-Cell Lymphoproliferative Disorder - CISMeF





Preferred Label : Primary Cutaneous Acral CD8-Positive T-Cell Lymphoproliferative Disorder;

NCIt synonyms : Primary Cutaneous Acral CD8-Positive T-Cell LPD; Primary Cutaneous Acral CD8-Positive T-Cell Lymphoma;

NCIt definition : A primary cutaneous T-cell lymphoproliferative disorder that presents as an acral (peripheral) lesion. It is composed of CD8-positive neoplastic T-lymphocytes. It is usually localized to a single site and has an indolent clinical course. Local or more extensive recurrences have been described in a minority of patients.;

Neoplastic status : Undetermined;

NCI Metathesaurus CUI : CL526531;

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29/07/2025


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