Indolent Clonal T-Cell Lymphoproliferative Disorder of the Gastrointestinal Tract - CISMeF
Indolent Clonal T-Cell Lymphoproliferative Disorder of the Gastrointestinal TractNCIt concept
Preferred Label : Indolent Clonal T-Cell Lymphoproliferative Disorder of the Gastrointestinal Tract;
NCIt synonyms : ITLPD-GI; Indolent T-Cell Lymphoproliferative Disorder of the Gastrointestinal Tract; Indolent T-Cell Lymphoma of the Gastrointestinal Tract;
NCIt related terms : Indolent T-cell lymphoproliferative disorder of gastrointestinal tract;
NCIt definition : A clonal T-cell lymphoproliferative disorder that can involve the mucosa in all sites
of the gastrointestinal tract, but is most common in the small intestine and colon.
The lymphoid cells infiltrate the lamina propria but usually do not show invasion
of the epithelium. The clinical course is indolent, but most patients do not respond
to conventional chemotherapy. A subset of cases progress to a higher-grade T-cell
lymphoma with spread beyond the gastrointestinal tract. (WHO 2017);