Lymphomatoid Papulosis with DUSP22-IRF4 Gene Rearrangement

Preferred Label : Lymphomatoid Papulosis with DUSP22-IRF4 Gene Rearrangement;

NCIt synonyms : LyP with Chromosome 6p25 Rearrangement; LyP with DUSP22-IRF4 Gene Rearrangement; Lymphomatoid Papulosis with Chromosome 6p25.3 Rearrangement; LyP with Chromosome 6p25.3 Rearrangement; Lymphomatoid Papulosis with DUSP22 Locus Rearrangement;

NCIt definition : A variant of lymphomatoid papulosis associated with chromosomal rearrangements involving the DUSP22-IRF4 locus at 6p25.3.;

Neoplastic status : Uncertain Malignant Potential;

NCI Metathesaurus CUI : CL526522;

Details

Origin ID

C139017;

UMLS CUI

C4528215;

Disease excludes abnormal cell
- Neoplastic B-Lymphocyte [NCIt concept]
Disease excludes normal cell origin
- Myeloid Cell [NCIt concept]
- Precursor Natural Killer Cell [NCIt concept]
- Precursor T-Lymphoblast [NCIt concept]
Disease may have findings
- Indolent Clinical Course [NCIt concept]
- Papular Lesion [NCIt concept]
- Skin Nodule [NCIt concept]
Has associated anatomic sites
- Hematopoietic and Lymphatic System [NCIt concept]
- Integumentary System [NCIt concept]
- Skin [NCIt concept]
Has cytogenetic abnormalities
- Rearrangement of 6p25.3 [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
disease_has_abnormal_cell
- Abnormal Hematopoietic and Lymphoid Cell [NCIt concept]
- Abnormal Lymphocyte [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Hematopoietic and Lymphoid Cell [NCIt concept]
- Neoplastic Lymphocyte [NCIt concept]
- Neoplastic T-Lymphocyte [NCIt concept]
- Neoplastic T-Lymphocyte and Neoplastic Natural Killer Cell [NCIt concept]
disease_has_finding
- Borderline Lesion [NCIt concept]
- CD30-Positive Neoplastic Cells Present [NCIt concept]
- Complete Regression [NCIt concept]
- Cutaneous Involvement [NCIt concept]
- Favorable Clinical Outcome [NCIt concept]
- Primary Lesion [NCIt concept]
disease_has_normal_cell_origin
- Activated Skin-Homing T-Lymphocyte [NCIt concept]
- Hematopoietic and Lymphoid Cell [NCIt concept]
- Lymphocyte [NCIt concept]
- Peripheral (Post-Thymic) T-Lymphocyte and Natural Killer Cell [NCIt concept]
- T-Lymphocyte and Natural Killer Cell [NCIt concept]
disease_has_normal_tissue_origin
- Hematopoietic and Lymphoid Tissue [NCIt concept]
- Lymphoid Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Hematopoietic and Lymphatic System [NCIt concept]
- Lymphatic System [NCIt concept]
- Skin [NCIt concept]
disease_may_have_cytogenetic_abnormality
- Clonal T-Cell Receptor Beta Chain Gene Rearrangement [NCIt concept]
- Clonal T-Cell Receptor Gamma Chain Gene Rearrangement [NCIt concept]
disease_may_have_molecular_abnormality
- Clonal T-Cell Receptor Beta Chain Gene Rearrangement [NCIt concept]
- Clonal T-Cell Receptor Gamma Chain Gene Rearrangement [NCIt concept]

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