" /> Uterine Corpus Malignant PEComa - CISMeF





Preferred Label : Uterine Corpus Malignant PEComa;

NCIt synonyms : Malignant Uterine Corpus Perivascular Epithelioid Cell Tumor; Malignant Uterine Corpus PEComa; Uterine Corpus Malignant Perivascular Epithelioid Cell Tumor;

NCIt definition : A malignant neoplasm with perivascular epithelioid cell differentiation arising from the uterine corpus. The neoplasm is usually a large size, and charcaterized by the presence of marked nuclear atypia, pleomorphism, increased mitotic activity, necrosis, and infiltrative margins. The most common metastatic sites are lungs, lymph nodes, and bone. Patients present with a pelvic mass or abnormal bleeding.;

Neoplastic status : Malignant;

NCI Metathesaurus CUI : CL508057;

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30/07/2025


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