Chronic Active EBV Disease

Preferred Label : Chronic Active EBV Disease;

NCIt synonyms : CAEBV Infection; CAEBV; Systemic CAEBV of T-and NK-Cell Type; Systemic Chronic Active EBV Infection of T-Cell and NK-Cell Type; Chronic Active EBV Infection; Chronic Active Epstein-Barr Virus Disease; Chronic Active EBV Infection of T-and NK-Cell Type, Systemic Form; Systemic Chronic Active EBV Disease;

NCIt related terms : Chronic active Epstein-Barr virus (without identified mutation);

NCIt definition : An EBV-positive T-cell/NK-cell lymphoproliferative disorder characterized by repeated infectious mononucleosis-like symptoms, a very high titer of anti-EBV antibodies, and high levels of Epstein-Barr virus nucleic acids. Patients often develop progressive cellular and humoral immunodeficiency with pancytopenia and hypogammaglobulinemia.;

Neoplastic status : Undetermined;

NCI Metathesaurus CUI : CL504910;

Details

Origin ID

C126348;

UMLS CUI

C4289792;

Disease excludes normal cell origin
- Myeloid Cell [NCIt concept]
Has associated anatomic sites
- Hematopoietic and Lymphatic System [NCIt concept]
Semantic type(s)
- Disease or Syndrome [UMLS semantic type]
concept_is_in_subset
- Cellosaurus Disease Terminology [NCIt concept]
- Cellosaurus Terminology [NCIt concept]
disease_has_abnormal_cell
- Abnormal Lymphocyte [NCIt concept]
disease_has_associated_disease
- EBV Infection [NCIt concept]
disease_has_finding
- Epstein-Barr Virus Positive [NCIt concept]
- Systemic Disease [NCIt concept]
disease_has_normal_cell_origin
- Hematopoietic and Lymphoid Cell [NCIt concept]
- Lymphocyte [NCIt concept]
- T-Lymphocyte and Natural Killer Cell [NCIt concept]
disease_has_normal_tissue_origin
- Hematopoietic and Lymphoid Tissue [NCIt concept]
- Lymphoid Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Hematopoietic and Lymphatic System [NCIt concept]
- Lymphatic System [NCIt concept]
disease_may_have_molecular_abnormality
- DDX3X Gene Mutation [NCIt concept]
- KMT2D Gene Mutation [NCIt concept]

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