Childhood Lymphomatoid Granulomatosis

Preferred Label : Childhood Lymphomatoid Granulomatosis;

NCIt definition : Lymphomatoid granulomatosis that occurs during childhood.;

Alternative definition : NICHD: An Epstein-Barr virus-associated B-cell lymphoproliferative disorder in children that nearly always affects the lungs, with skin involvement in 50% of the cases. Morphologically, three grades are recognized: grade I, II, and III.;

Neoplastic status : Uncertain Malignant Potential;

Details

Origin ID

C123392;

UMLS CUI

C4055244;

Disease excludes abnormal cell
- Neoplastic T-Lymphocyte and Neoplastic Natural Killer Cell [NCIt concept]
Disease excludes normal cell origin
- Myeloid Cell [NCIt concept]
- Precursor B-Lymphoblast [NCIt concept]
Disease may have findings
- Fever [NCIt concept]
- Malaise [NCIt concept]
- Musculoskeletal Pain [NCIt concept]
- Weight Loss [NCIt concept]
Has associated anatomic sites
- Hematopoietic and Lymphatic System [NCIt concept]
- Lymphatic System [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
concept_is_in_subset
- NICHD Terminology [NCIt concept]
- Pediatric Hematology-Oncology Terminology [NCIt concept]
disease_has_abnormal_cell
- Abnormal Hematopoietic and Lymphoid Cell [NCIt concept]
- Abnormal Lymphocyte [NCIt concept]
- Neoplastic B-Lymphocyte [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Hematopoietic and Lymphoid Cell [NCIt concept]
- Neoplastic Lymphocyte [NCIt concept]
disease_has_associated_disease
- EBV Infection [NCIt concept]
disease_has_finding
- Angiocentric Pattern [NCIt concept]
- Angiodestructive Pattern [NCIt concept]
- Borderline Lesion [NCIt concept]
- Childhood Lesion [NCIt concept]
- Chronic Inflammatory Infiltrate [NCIt concept]
- Epstein-Barr Virus Positive [NCIt concept]
disease_has_normal_cell_origin
- B-Lymphocyte [NCIt concept]
- EBV-Transformed Mature B-Lymphocyte [NCIt concept]
- Hematopoietic and Lymphoid Cell [NCIt concept]
- Lymphocyte [NCIt concept]
- Mature B-Lymphocyte [NCIt concept]
- Mature Lymphocyte [NCIt concept]
disease_has_normal_tissue_origin
- Hematopoietic and Lymphoid Tissue [NCIt concept]
- Lymphoid Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Hematopoietic and Lymphatic System [NCIt concept]
- Lymphatic System [NCIt concept]

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