Malignant PEComa

Preferred Label : Malignant PEComa;

NCIt related terms : Perivascular epithelioid cell tumor, malignant; PEComa, malignant;

NCIt definition : A usually large and aggressive tumor with perivascular epithelioid cell differentiation characterized by the presence of marked nuclear atypia, pleomorphism, increased mitotic activity, necrosis, and infiltrative margins. The most common metastatic sites are liver, lungs, lymph nodes, and bone.;

Neoplastic status : Malignant;

Details

Origin ID

C121792;

UMLS CUI

C3839062;

Automatic exact mappings (from CISMeF team)
- Perivascular epithelioid tumor, malignant (morphologic abnormality) [SNOMED CT concept]
- Perivascular epithelioid tumour, malignant [ICD-11 Extension code]
Disease may have findings
- Aggressive Clinical Course [NCIt concept]
Excludes anatomical site(s)
- Bone [NCIt concept]
Has associated anatomic sites
- Connective and Soft Tissue [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Perivascular epithelioid tumor, malignant (morphologic abnormality) [SNOMED CT concept]
concept_is_in_subset
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology Terminology [NCIt concept]
- Mapped ICDO3.2 Terminology [NCIt concept]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
- Indolent Clinical Course [NCIt concept]
disease_has_abnormal_cell
- Malignant Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Perivascular Epithelioid Cell [NCIt concept]
disease_has_finding
- Cellular Pleomorphism [NCIt concept]
- HMB-45-Positive Neoplastic Cells Present [NCIt concept]
- High Mitotic Activity [NCIt concept]
- Infiltrative Growth Pattern [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
- Marked Nuclear Atypia Present [NCIt concept]
- Metastatic/Recurrent Disease [NCIt concept]
- Necrotic Change [NCIt concept]
- Perivascular Arrangement of Tumor Cells [NCIt concept]
- S-100-Positive Neoplastic Cells Present [NCIt concept]
- Tissue Differentiation Uncertain [NCIt concept]
disease_has_normal_tissue_origin
- Soft Tissue [NCIt concept]
disease_mapped_to_gene
- TSC2 Gene [NCIt concept]
disease_may_have_molecular_abnormality
- TSC2 Gene Mutation [NCIt concept]

Keyword's position in hierarchy(ies) :

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