" /> 4a-hydroxy-erythro-5,6,7,8-tetrahydrobiopterin dehydratase - CISMeF





Preferred Label : 4a-hydroxy-erythro-5,6,7,8-tetrahydrobiopterin dehydratase;

MeSH note : converts (6R)-L-erythro-5,6,7,8-tetrahydrobiopterin to quinoid dihydropterin; defect in Hermansky-Pudlak syndromeresults in decreased levels of biopterin;

MeSH synonym : 4a-OH-6BH4-dehydratase; 4a-hydroxy-6BH4-dehydratase;

Registry Number MeSH : EC 4.2.1.-;

Is substance : O;

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02/05/2025


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