Preferred Label : 4a-hydroxy-erythro-5,6,7,8-tetrahydrobiopterin dehydratase;
MeSH note : converts (6R)-L-erythro-5,6,7,8-tetrahydrobiopterin to quinoid dihydropterin; defect
in Hermansky-Pudlak syndromeresults in decreased levels of biopterin;
MeSH synonym : 4a-OH-6BH4-dehydratase; 4a-hydroxy-6BH4-dehydratase;
Registry Number MeSH : EC 4.2.1.-;
Is substance : O;
Origin ID : C114534;
UMLS CUI : C0757627;
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